Book contents
- International Compendium of Movement Disorders
- International Compendium of Movement Disorders
- Copyright page
- Contents
- Contributors
- International Compendium of Movement Disorders
- Hypo- and Hyperkinetic, Dyscoordinative and Otherwise Inappropriate Motor and Behavioral Movement Disorders
- Section 1: Basic Introduction
- Section 2: Hypokinetic Movement Disorders
- Section 3: Hyperkinetic Movement Disorders
- Section 4: Dyscoordinative and Otherwise Inappropriate Motor Behaviors
- Chapter 46 Ataxia
- Chapter 47 Treatable Hereditary Cerebellar Ataxias
- Chapter 48 Gait and Balance Disorders
- Chapter 49 Episodic/Paroxysmal Movement Disorders
- Chapter 50 Sleep-Related Movement Disorders and Disturbances of Motor Control
- Chapter 51 Drug-Induced Movement Disorders
- Chapter 52 Psychiatric Movement Disorders
- Chapter 53 Functional Movement Disorders
- Section 5: Objectifying Movement Disorders
- Movement Disorders in Vivo: Video Fragments
- Acronyms and Abbreviations
- Index
- References
Chapter 46 - Ataxia
from Section 4: - Dyscoordinative and Otherwise Inappropriate Motor Behaviors
Published online by Cambridge University Press: 07 January 2025
Book contents
- International Compendium of Movement Disorders
- International Compendium of Movement Disorders
- Copyright page
- Contents
- Contributors
- International Compendium of Movement Disorders
- Hypo- and Hyperkinetic, Dyscoordinative and Otherwise Inappropriate Motor and Behavioral Movement Disorders
- Section 1: Basic Introduction
- Section 2: Hypokinetic Movement Disorders
- Section 3: Hyperkinetic Movement Disorders
- Section 4: Dyscoordinative and Otherwise Inappropriate Motor Behaviors
- Chapter 46 Ataxia
- Chapter 47 Treatable Hereditary Cerebellar Ataxias
- Chapter 48 Gait and Balance Disorders
- Chapter 49 Episodic/Paroxysmal Movement Disorders
- Chapter 50 Sleep-Related Movement Disorders and Disturbances of Motor Control
- Chapter 51 Drug-Induced Movement Disorders
- Chapter 52 Psychiatric Movement Disorders
- Chapter 53 Functional Movement Disorders
- Section 5: Objectifying Movement Disorders
- Movement Disorders in Vivo: Video Fragments
- Acronyms and Abbreviations
- Index
- References
Summary
"Ataxia" refers to both the neurologic syndrome of motor coordination and to a large and diverse group of diseases that have motor coordination impairment as their main clinical feature. The brain structure most consistently affected is the cerebellum. Although many different brain diseases may manifest with ataxia, the vast majority of slowly progressive ataxias are genetic diseases. Indeed, genetic molecular analysis has become the cornerstone of both diagnosis and classification of this complex group of conditions. In this overview, the basics of the clinical features and the classification of these diseases, as well as common conditions, and recently defined novel forms of ataxia are discussed.
Keywords
- Type
- Chapter
- Information
- International Compendium of Movement Disorders , pp. 568 - 591Publisher: Cambridge University PressPrint publication year: 2025
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