Book contents
- Congenital Cardiac Anesthesia
- Congenital Cardiac Anesthesia
- Copyright page
- Dedication
- Contents
- Contributors
- Introduction
- Chapter 1 A Congenital Heart Disease Primer
- Section 1 Left-to-Right Shunts
- Section 2 Right-Sided Obstructive Lesions
- Section 3 Left-Sided Obstructive Lesions
- Section 4 Complex Mixing Lesions
- Section 5 Single-Ventricle Physiology
- Section 6 Heart Failure, Mechanical Circulatory Support, and Transplantation
- Section 7 Miscellaneous Lesions and Syndromes
- Chapter 40 Idiopathic Pulmonary Hypertension
- Chapter 41 Pulmonary Hypertension and Congenital Heart Disease
- Chapter 42 Pulmonary Hypertension and Prematurity
- Chapter 43 Pulmonary Hypertension and Moyamoya Disease
- Chapter 44 Vascular Ring
- Chapter 45 Pericardial Effusion
- Chapter 46 Kawasaki Disease
- Chapter 47 VACTERL Syndrome
- Chapter 48 Hurler Syndrome
- Chapter 49 Long QT Syndrome
- Chapter 50 Marfan Syndrome
- Index
- References
Chapter 44 - Vascular Ring
from Section 7 - Miscellaneous Lesions and Syndromes
Published online by Cambridge University Press: 09 September 2021
Book contents
- Congenital Cardiac Anesthesia
- Congenital Cardiac Anesthesia
- Copyright page
- Dedication
- Contents
- Contributors
- Introduction
- Chapter 1 A Congenital Heart Disease Primer
- Section 1 Left-to-Right Shunts
- Section 2 Right-Sided Obstructive Lesions
- Section 3 Left-Sided Obstructive Lesions
- Section 4 Complex Mixing Lesions
- Section 5 Single-Ventricle Physiology
- Section 6 Heart Failure, Mechanical Circulatory Support, and Transplantation
- Section 7 Miscellaneous Lesions and Syndromes
- Chapter 40 Idiopathic Pulmonary Hypertension
- Chapter 41 Pulmonary Hypertension and Congenital Heart Disease
- Chapter 42 Pulmonary Hypertension and Prematurity
- Chapter 43 Pulmonary Hypertension and Moyamoya Disease
- Chapter 44 Vascular Ring
- Chapter 45 Pericardial Effusion
- Chapter 46 Kawasaki Disease
- Chapter 47 VACTERL Syndrome
- Chapter 48 Hurler Syndrome
- Chapter 49 Long QT Syndrome
- Chapter 50 Marfan Syndrome
- Index
- References
Summary
A vascular ring is a congenital malformation of the aorta and its branch vessels in which the esophagus and/or tracheobronchial tree are either completely (complete ring) or partially (incomplete ring) encircled by vascular structures and/or their atretic remnants, resulting in mechanical obstruction of these structures and resultant symptomatology. Vascular rings result from abnormal segmental regression and/or persistence of portions of the embryonic aortic arch complex. Infants may present with recurrent upper respiratory infections or pneumonia, wheezing, stridor, slow feeding, gastroesophageal reflux or vomiting, and/or failure to thrive. In children and older patients, the symptoms are similar to those seen in infancy with the addition of dysphagia to solids. Surgical division of a vascular ring is indicated when symptoms of airway and/or esophageal compression are present and is generally performed without delay once a diagnosis is made. This chapter highlights the perioperative anesthetic challenges in caring for a child for airway evaluation of a suspected vascular ring.
Keywords
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- Congenital Cardiac AnesthesiaA Case-based Approach, pp. 338 - 344Publisher: Cambridge University PressPrint publication year: 2021
References
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Suggested Reading
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