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Benign Hereditary Chorea a Case Report

Published online by Cambridge University Press:  02 January 2018

S. J. Loosmore  and
K. Wood
S. J. Loosmore*
Affiliation:
Midland Nerve Hospital
K. Wood
Affiliation:
John Conolly Hospital, Birmingham
*
Elvetham Road, Edgbaston, Birmingham B15 2NJ
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Abstract

A case of benign hereditary chorea is reported, along with a brief review of the condition. It is a rare and little known autosomal dominant disorder which may be confused with Huntington's chorea, which has a more serious prognosis. The case described shows some characteristic features. It is difficult to decide how many of the patient's psychiatric difficulties are a reaction to his disabilities and how many have an organic substrate.

Type
Brief Reports
Information
The British Journal of Psychiatry , Volume 152 , Issue 1 , January 1988 , pp. 131 - 134
Copyright
Copyright © The Royal College of Psychiatrists 

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References

Bird, T. D., Carlson, C. B. & Hall, J. G. (1976) Familial essential (‘benign’) chorea. Journal of Medical Genetics, 13, 357–362.Google Scholar
Chun, R. W., Daly, R. F., Mansheim, B. J. & Wolcott, G. J. (1973) Benign familial chorea with onset in childhood. Journal of the American Medical Association, 225, 1603–1607.Google Scholar
Haerer, A. F., Currier, R. D. & Jackson, J. F. (1967) Hereditary nonprogressive chorea of early onset. New England Journal of Medicine, 276, 1220–1224.Google Scholar
Harper, P. S. (1978) Benign hereditary chorea: clinical and genetic aspects. Clinical Genetics, 13, 85–95.Google Scholar
Leli, D. A., Furlow, T. W. & Falgout, J. C. (1984) Benign familial chorea: an association with intellectual impairment. Journal of Neurology, Neurosurgery, and Psychiatry, 47, 471–474.Google Scholar
Nutting, P. A., Cole, B. R. & Schimke, R. N. (1969) Benign, recessively inherited choreo-athetosis of early onset. Journal of Medical Genetics, 6, 408–410.Google Scholar
Pincus, J. H. & Chutorian, A. M. (1966) Familial benign chorea - a new entity. Transactions of the American Neurological Association, 91, 319–321.Google Scholar
Pincus, J. H. & Chutorian, A. M. (1967) Familial benign chorea with intention tremor: a clinical entity. Journal of Pediatrics, 70, 724–729.Google Scholar
Robinson, R. O. & Thornett, C. E. (1985) Benign hereditary chorea - response to steroids. Developmental Medicine and Child Neurology, 27, 814–821.Google Scholar
De Silva, L. (1977) Biochemical mechanisms and management of choreiform movement disorders. Drugs, 14, 300–310.Google Scholar
Sleigh, G. & Lindenbaum, R. H. (1981) Benign (non-paroxysmal) familial chorea: paediatric perspectives. Archives of Diseases in Childhood, 56, 616–621.Google Scholar
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