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Superior semicircular canal dehiscence syndrome: a new aetiology

Published online by Cambridge University Press:  08 March 2017

P Puwanarajah ,
P Pretorius  and
I Bottrill
P Puwanarajah
Affiliation:
Department of Otolaryngology, John Radcliffe Hospital, Oxford, UK
P Pretorius
Affiliation:
Department of Neuroradiology, John Radcliffe Hospital, Oxford, UK
I Bottrill*
Affiliation:
Department of Otolaryngology, John Radcliffe Hospital, Oxford, UK
*
Address for correspondence: Mr I Bottrill, Consultant Otolaryngologist, Department of Otolaryngology, John Radcliffe Hospital, Oxford OX3 9DU, UK. E-mail: [email protected]
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Abstract

Objective:

We report what we believe to be a unique aetiology of the superior semicircular canal dehiscence syndrome, a recently described condition in which vestibular imbalance and/or hearing loss results from the loss of continuity of the bone overlying the superior semicircular canals.

Case report:

A 58-year-old woman presented with autophony in the right ear and momentary imbalance when shouting (Tullio phenomenon). Temporal bone computed tomography revealed a defect of the right superior semicircular canal caused by an enlarged superior petrosal sinus receiving drainage from a large cerebellar developmental venous anomaly.

Conclusions:

We review superior semicircular canal dehiscence syndrome and its management, and we discuss common aetiologies, contrasting these with the unusual aetiology presented here. We conclude that superior semicircular canal dehiscence syndrome may present with a solely developmental aetiology, despite presenting late in life.

Keywords

Semicircular CanalsPetrosal SinusVertigo
Type
Clinical Record
Information
The Journal of Laryngology & Otology , Volume 122 , Issue 7 , July 2008 , pp. 741 - 744
Copyright
Copyright © JLO (1984) Limited 2008

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References

1 Minor, LB, Solomon, D, Zinreich, JS, Zee, DS. Sound- and/or pressure-induced vertigo due to bone dehiscence of the superior semicircular canal. Arch Otolaryngol Head Neck Surg 1998;124:249–58CrossRefGoogle ScholarPubMed
2 Carey, JP, Minor, LB, Nager, GT. Dehiscence or thinning of bone overlying the superior semicircular canal in a temporal bone survey. Arch Otolaryngol Head Neck Surg 2000;126:137–47CrossRefGoogle ScholarPubMed
3 Krombach, GA, DiMartino, E, Schmitz-Rode, T, Prescher, A, Haage, P, Kinzel, S et al. Posterior semicircular canal dehiscence: a morphological cause of vertigo similar to superior semicircular canal dehiscence. Eur Radiol 2003;13:1444–50CrossRefGoogle ScholarPubMed
4 Minor, LB. Clinical manifestations of superior semicircular canal dehiscence. Laryngoscope 2005;115:1717–27CrossRefGoogle ScholarPubMed
5 Carey, JP, Hirvonen, TP, Hullar, TE, Minor, LB. Acoustic responses of vestibular afferents in a model of superior canal dehiscence. Otol Neurol 2004;25:345–52CrossRefGoogle Scholar
6 Hirvonen, TP, Carey, JP, Liang, CJ, Minor, LB. Superior canal dehiscence: mechanism of pressure sensitivity in a chinchilla model. Arch Otolaryngol Head Neck Surg 2001;127:1331–6CrossRefGoogle Scholar
7 Tullio, P, I riflessi Sonori. Am J Physiol 1929;90:542–3Google Scholar
8 da Cuhna, Ferreira Suzane, de Melo Tavares de, Lima Marco Antonio. Superior Canal Dehiscence Syndrome. Rev Bras Otorrinolaringol 2006;72:414–8Google Scholar
9 Minor, LB. The superior semicircular canal dehiscence syndrome. Am J Otol 2000;21:9–19CrossRefGoogle Scholar
10 Carey, JP, Migliaccio, AA, Minor, LB. Semicircular canal function before and after surgery for superior canal dehiscence. Otol Neurol 2007;28:356–64CrossRefGoogle ScholarPubMed