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Feingold syndrome – a cause of profound deafness

Published online by Cambridge University Press:  29 June 2007

Annabel Dodds ,
Richard Ramsden  and
Helen Kingston
Annabel Dodds*
Affiliation:
East Lancashire Paediatric Audiology Service, Nelson, Manchester Royal Infirmary, Manchester, UK
Richard Ramsden
Affiliation:
Department of Otolaryngology, Manchester Royal Infirmary, Manchester, UK
Helen Kingston
Affiliation:
Regional Genetic Service, St Mary's Hospital, Manchester, UK
*
Address for correspondence: Dr Annabel A. Dodds, M.B.Ch.B., M.Sc., Consultant Community Paediatrician in Audiology, East Lancashire Paediatric Audiology Service, Audiology Clinic, Leeds Road, Nelson BB9 9TG
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Abstract

A case of Feingold syndrome is presented with a previously undescribed association of bilateral profound hearing impairment. Computed tomography (CT) scanning revealed severe narrowing of the internal auditory meatuses at the peripheral end with non-existent auditory nerves. This pathology is significant in the future habilitation of the child, as cochlear implantation is not possible. Children with multiple congenital anomalies should have radiological investigations before hopes are raised with respect to cochlear implantation.

Keywords

DeafnessCochlear implant
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 113 , Issue 10 , October 1999 , pp. 919 - 921
Copyright
Copyright © JLO (1984) Limited 1999

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References

Brunner, H. G., Winter, R. M. (1991) Autosomal dominant inheritance of abnormalities of the hands and feet with short palpebral fissures, variable microcephaly with learning disability, and oesophageal/duodenal atresia. Journal of Medical Genetics 28: 389–394.CrossRefGoogle ScholarPubMed
Feingold, M. (1975) Case report 30. Syndrome Identification 3(1): 16–17.Google Scholar
Feingold, M. (1978) An unusual microcephaly. Hospital Practice 13: 44–49.CrossRefGoogle ScholarPubMed
König, R., Selzer, G., Stolp, A., Fuchs, S. (1990) Microcephaly, mesobrachyphalangy and tracheoesophageal fistula: MMT syndrome. Dysmorphology and Clinical Genetics 4(3): 83–86.Google Scholar
Schinzel, A. (1984) Chromosome 13 deletions. In Catalogue of Unbalanced Chromosome Aberrations in Man. De Gruyter, Berlin, pp 485–489.Google Scholar
Phelps, P. (1998) Imaging for cochlear implants: the importance of the latest techniques for pre-operative assessment. Journal of Audiological Medicine 7(3): 145–154.Google Scholar