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Congenital cholesteatoma of mastoid region manifesting as acute mastoiditis: case report and literature review

Published online by Cambridge University Press:  11 December 2009

H Hidaka ,
E Ishida ,
K Kaku ,
H Nishikawa  and
T Kobayashi
H Hidaka*
Affiliation:
Department of Otolaryngology-Head and Neck Surgery, Tohoku University Graduate School of Medicine, Sendai, Japan
E Ishida
Affiliation:
Department of Otolaryngology, Iwaki Kyoristu General Hospital, Fukushima, Japan
K Kaku
Affiliation:
Department of Otolaryngology, Iwaki Kyoristu General Hospital, Fukushima, Japan
H Nishikawa
Affiliation:
Department of Otolaryngology, Iwaki Kyoristu General Hospital, Fukushima, Japan
T Kobayashi
Affiliation:
Department of Otolaryngology-Head and Neck Surgery, Tohoku University Graduate School of Medicine, Sendai, Japan
*
Address for correspondence: Dr Hiroshi Hidaka, Department of Otolaryngology-HNS, Tohoku University Graduate School of Medicine, 1-1 Seiryomachi, Aoba-ku, Sendai 980-8575, Japan. Fax: +81 22 717 7307 E-mail: [email protected]
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Abstract

Objectives:

We report an extremely rare case of congenital cholesteatoma of the mastoid region, presenting as acute mastoiditis. We also review the 16 previously reported cases of congenital cholesteatoma of the mastoid region.

Case report:

A 65-year-old man presented with left-sided, post-auricular swelling and pain. Acute mastoiditis was diagnosed, with computed tomography demonstrating destruction of the bony plates of the posterior cranial fossa and sigmoid sinus. Initial surgery revealed a cholesteatoma in the mastoid, with no extension into the aditus ad antrum or attic. These findings were confirmed by pathological and immunohistochemical analysis of the surgical specimen, the latter using involucrin. The cholesteatoma matrix was completely removed in a second operation.

Conclusions:

Including this case, only four of the 17 reported cases of congenital cholesteatoma of the mastoid region showed post-auricular pain or swelling, indicating acute mastoiditis. Clinicians should bear in mind that congenital cholesteatoma may be present in patients presenting with mastoiditis, particularly adults.

Keywords

CholesteatomaCongenitalMastoiditisTemporal Bone
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 124 , Issue 7 , July 2010 , pp. 810 - 815
Copyright
Copyright © JLO (1984) Limited 2009

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