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Unilateral hearing loss due to a rhabdomyoma in a six-year-old child

Published online by Cambridge University Press:  29 June 2007

J. P. P. M. van Leeuwen ,
M. Pruszczynski ,
H. A. M. Marres ,
J. A. Grotenhuis  and
C. W. R. J. Cremers
J. P. P. M. van Leeuwen*
Affiliation:
Department of Otorhinolaryngology, University Hospital Nijmegen, The Netherlands.
M. Pruszczynski
Affiliation:
Department of Pathology, University Hospital Nijmegen, The Netherlands.
H. A. M. Marres
Affiliation:
Department of Otorhinolaryngology, University Hospital Nijmegen, The Netherlands.
J. A. Grotenhuis
Affiliation:
Department of Neurosurgery, University Hospital Nijmegen, The Netherlands.
C. W. R. J. Cremers
Affiliation:
Department of Otorhinolaryngology, University Hospital Nijmegen, The Netherlands.
*
J. P. P. M. van Leeuwen, Dept of Otorhinolaryngology, University Hospital Nijmegen, P0 Box 9101,6500 HB Nijmegen, The Netherlands. Fax: (80) 540251
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Abstract

A case report of a six-year-old child is presented, who had had a unilateral sensorineural hearing loss for several years. Because of impairment in the ABR as well as in the caloric testing a MRI and CT scan were performed. A 17 mm tumour in the cerebellopontine angle (CPA) was detected, which after suboccipital surgery proved to be a rhabdomyoma. This tumour has not been described before in the CPA. Unilateral sensorineural hearing loss should, at all ages, be an indication for further (radiodiagnostic) investigations.

Keywords

RhabdomyomHearing loss, unilateralCerebello-pontine angleChild
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 109 , Issue 12 , December 1995 , pp. 1186 - 1189
Copyright
Copyright © JLO (1984) Limited 1995

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