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Cochlear implant failure due to unexpected absence of the eighthnerve – a cautionary tale

Published online by Cambridge University Press:  29 June 2007

R. F. Gray ,
J. Ray ,
D. M. Baguley ,
Z. Vanat ,
J. Begg  and
P. D. Phelps
R. F. Gray*
Affiliation:
East of England Cochlear Implant Centre, Addenbrooke' Hospital, Cambridge and the Royal National Throat Noseand Ear Hospital, London, UK.
J. Ray
Affiliation:
East of England Cochlear Implant Centre, Addenbrooke' Hospital, Cambridge and the Royal National Throat Noseand Ear Hospital, London, UK.
D. M. Baguley
Affiliation:
East of England Cochlear Implant Centre, Addenbrooke' Hospital, Cambridge and the Royal National Throat Noseand Ear Hospital, London, UK.
Z. Vanat
Affiliation:
East of England Cochlear Implant Centre, Addenbrooke' Hospital, Cambridge and the Royal National Throat Noseand Ear Hospital, London, UK.
J. Begg
Affiliation:
East of England Cochlear Implant Centre, Addenbrooke' Hospital, Cambridge and the Royal National Throat Noseand Ear Hospital, London, UK.
P. D. Phelps
Affiliation:
East of England Cochlear Implant Centre, Addenbrooke' Hospital, Cambridge and the Royal National Throat Noseand Ear Hospital, London, UK.
*
Address for correspondence: Mr R. F. Gray, M.A., F.R.C.S., Clinic 10, Box 48, Addenbrooke's Hospital, Hills Road, Cambridge, CB2 2QQ.
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Abstract

We present a case of bilateral absence of the eighth cranial nerve in the internal auditory meatus (IAM). This caused total failure of responses after cochlear implantation in a six-year-old patient with congenital deafness. Pre-operative magnetic resonance (MR)imaging is important to show not only the anatomy of the middle and inner ears but also the structures in the IAM.

Keywords

Cochlear implantHearing losssensorineuralcongenitalEar, anatomyMagnetic resonance imaging
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 112 , Issue 7 , July 1998 , pp. 646 - 649
Copyright
Copyright © JLO (1984) Limited 1998

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