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Successful use of calcium channel blocker for management of arterio-venous malformations following Fontan procedure

Published online by Cambridge University Press:  29 August 2018

Ramzi Hamzeh ,
Ziad Bulbul  and
Jana Assy
Ramzi Hamzeh
Affiliation:
Department of Pediatric and Adolescent Medicine, American University of Beirut Medical Center, Beirut, Lebanon
Ziad Bulbul
Affiliation:
Department of Pediatric and Adolescent Medicine, American University of Beirut Medical Center, Beirut, Lebanon
Jana Assy*
Affiliation:
Department of Pediatric and Adolescent Medicine, American University of Beirut Medical Center, Beirut, Lebanon
*
Author for correspondence: J. Assy, Department of Pediatric and Adolescent Medicine, American University of Beirut Medical Center, P.O. Box 11-0236, Riad El Solh, Beirut 1107-2020, Lebanon. Tel: 009611350000; E-mail: [email protected]
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Abstract

In diffuse forms of arteriovenous malformation following Fontan procedure, “classical” medical therapy, inhaled nitric oxide and sildenafil, may play a role, until re-direction of hepatic flow to pulmonary circulation cures it. However, in refractory cases, as reported in our 2-year-old patient, unusual medications such as calcium channel blockers can be tried and continued if patients respond adequately.

Keywords

Arteriovenous malformationsFontanamlodipinehypoxemiaintensive care
Type
Brief Report
Information
Cardiology in the Young , Volume 28 , Issue 12 , December 2018 , pp. 1468 - 1470
Copyright
© Cambridge University Press 2018 

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