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Prenatal diagnosis of tricuspid valvar dysplasia and regurgitation—always a poor outcome?

Published online by Cambridge University Press:  19 August 2008

Enrico Chiappa ,
Piero Gaglioti  and
Tullia Todros
Enrico Chiappa*
Affiliation:
From the Divisione di Cardiologia Pediatrica, Ospedale Infantile Regina Margherita Torino
Piero Gaglioti
Affiliation:
Divisione di Cardiologia Pediatrica, Istituto di Ginecologia e Ostetricia dell' Universitá di Torino, Torino
Tullia Todros
Affiliation:
Divisione di Cardiologia Pediatrica, Istituto di Ginecologia e Ostetricia dell' Universitá di Torino, Torino
*
Dr. Enrico Chiappa, Divisione di Cardiologia Pediatrica, Ospedale Infantile Regina Margherita, Piazza Polonia 94, 10126 Torino, Italy. Tel. 0039 11 673281 or 6927253; Fax. 6635168.
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Abstract

The anatomic and pathophysiologic features of tricuspid valvar dysplasia are discussed in the light of two cases observed during fetal life which progressed with an unexpectedly favorable course. Some fetal echocardiographic features are proposed to explain this outcome. First, absence of associated cardiovascular abnormalities; second, clear separation between well represented right ventricular walls and the tricuspid valvar leaflets; third, normal proximal insertion of the tricuspid leaflets and, fourth, normal dimensions of the pulmonary trunk. We recommend karyotyping because of the possible association of this malformation with an aneuploid karyotype. We also describe transitory functional atresia of the pulmonary valve at birth, as far as we know for the first time, in a neonate that had normal forward flow of blood as seen on Doppler sampling in fetal life.

Keywords

Fetal cardiologyfetal heart measurementscongenital heart diseasetricuspid valve insufficiency
Type
Original Manuscripts
Information
Cardiology in the Young , Volume 5 , Issue 4 , October 1995 , pp. 338 - 344
Copyright
Copyright © Cambridge University Press 1995

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