Hostname: page-component-586b7cd67f-2brh9 Total loading time: 0 Render date: 2024-11-24T13:50:28.804Z Has data issue: false hasContentIssue false
  • English
  • Français

Progressive fetal atrioventricular block in heterotaxy syndrome

Published online by Cambridge University Press:  18 June 2007

Sethuraman Swaminathan  and
Anitha Parthiban
Sethuraman Swaminathan*
Affiliation:
Division of Cardiology, Department of Pediatrics, University of Miami-Miller School of Medicine, Miami, Florida, Unites States of America
Anitha Parthiban
Affiliation:
Division of Cardiology, Department of Pediatrics, University of Miami-Miller School of Medicine, Miami, Florida, Unites States of America
*
Correspondence to: Sethuraman Swaminathan, MD, Department of Pediatrics (Cardiology), University of Miami Miller School of Medicine, PO Box 016960 (R-76), Miami, Florida 33101, USA. Tel: +(305) 585 6683; Fax: +(305) 324 6012; E-mail: [email protected]
Get access Rights & Permissions [Opens in a new window]

Abstract

We report a fetus with left isomerism, in whom the atrioventricular block progressed from low grade second degree to complete block and fetal hydrops. While it is known that there is a high incidence of heart block in the fetus with left isomerism, as far as we are aware, ours is the first report of Wenckebach type block documented in the fetus by Doppler echocardiography, and demonstration of the progression of heart block during fetus life in the setting of left isomerism.

Keywords

Wenckebach phenomenonfetal echocardiogramleft isomerism
Type
Brief Report
Information
Cardiology in the Young , Volume 17 , Issue 4 , August 2007 , pp. 432 - 434
Copyright
Copyright © Cambridge University Press 2007

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1. Peoples, WM, Moller, JH, Edwards, JE. Polysplenia: a review of 146 cases. Pediatr Cardiol 1983; 4: 129–137.CrossRefGoogle ScholarPubMed
2. Ho, SY, Cook, A, Anderson, RH, Allan, LD, Fagg, N. Isomerism of the atrial appendages in the fetus. Pediatr Pathol 1991; 11: 589–608.CrossRefGoogle ScholarPubMed
3. Gilljam, T, McCrindle, B, Smallhorn, J, Williams, WG. Outcomes of left atrial isomerism over a 28-year period at a single institution. J Am Coll Cardiol 2000; 36: 908–916.CrossRefGoogle Scholar
4. Berg, C, Geipel, A, Smrcek, J, et al. . Prenatal diagnosis of cardiosplenic syndromes: a 10 year experience. Ultrasound Obstet Gynecol 2003; 22: 451–459.CrossRefGoogle ScholarPubMed
5. Sheley, RC, Nyberg, DA, Kapur, R. Azygous continuation of the interrupted inferior vena cava: a clue to prenatal diagnosis of the cardiosplenic syndromes. J Ultrasound Med 1995; 14: 381–387.CrossRefGoogle ScholarPubMed
6. Chitayat, D, Lao, A, Wilson, RD, Fagerstrom, C, Hayden, M. Prenatal diagnosis of asplenia/polysplenia syndrome. Am J Obstet Gynecol 1988; 158: 1085–1087.CrossRefGoogle ScholarPubMed
7. Machado, MVL, Tynan, MY, Curry, PVL, Allan, LD. Fetal complete heart block. Br Heart J 1988; 60: 512–515.CrossRefGoogle ScholarPubMed
8. Schmidt, KG, Ulmer, HE, Silverman, NH, Kleinman, CS, Copel, JA. Perinatal outcome of fetal complete atrioventricular block: a multicenter experience. J Am Coll Cardiol 1991; 17: 1360–1366.CrossRefGoogle ScholarPubMed
9. Shenker, L, Reed, KL, Anderson, CF, Marx, GR, Sobonya, RE, Graham, AR. Congenital heart block and cardiac anomalies in the absence of maternal connective tissue disease. Am J Obstet Gynecol 1987; 157: 248–253.CrossRefGoogle ScholarPubMed
10. Chan, FY, Woo, SK, Ghosh, A, Tang, M, Lam, C. Prenatal diagnosis of congenital fetal arrhythmias by simultaneous pulsed Doppler velocitometry of the fetal abdominal aorta and inferior vena cava. Obstetr Gynecol 1990; 76: 200–205.Google Scholar