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Neonatal surgical reconstruction and peri-operative care for hypoplastic left heart syndrome: current strategies

Published online by Cambridge University Press:  13 December 2011

Stephanie Fuller ,
Nancy Ghanayem ,
Paul Chai ,
John Nigro ,
Thomas Kleisli  and
Sarah Tabbutt
Stephanie Fuller*
Affiliation:
Cardiac Surgery, Children's Hospital of Philadelphia, Philadelphia, Pennsylvania, United States of America
Nancy Ghanayem
Affiliation:
Division of Pediatric Critical Care Medicine, Children's Hospital of Wisconsin and Medical College of Wisconsin, Milwaukee, Wisconsin, United States of America
Paul Chai
Affiliation:
The Congenital Heart Institute of Florida (CHIF), All Children's Hospital, Saint Petersburg and Tampa, Florida, United States of America
John Nigro
Affiliation:
Cardiac Surgery, Phoenix Children's Hospital and St. Joseph's Hospital and Medical Center, Phoenix, Arizona, United States of America
Thomas Kleisli
Affiliation:
Phoenix Children's Hospital and St. Joseph's Hospital and Medical Center, Phoenix, Arizona, United States of America
Sarah Tabbutt
Affiliation:
Division of Pediatric Critical Care Medicine, Benioff Children's Hospital, University of California, San Francisco, United States of America
*
Correspondence to: Dr Stephanie Fuller, MD, Cardiac Surgery, The Children's Hospital of Philadelphia, Philadelphia, Pennsylvania, United States of America. Tel: 215-590-2708; Fax: 215-590-2715; E-mail: [email protected]
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Abstract

The management of newborns with hypoplastic left heart syndrome has changed significantly over the past three decades, with an associated dramatic improvement in outcomes. The aim of this paper is to discuss current peri-operative and palliative surgical strategies. Owing to the fact that comparative outcomes for these strategies have been addressed in a limited number of prospective trials and extractions from multi-centred databases, the primary focus of this review is descriptive.

Keywords

Hypoplastic left heart syndromecongenital cardiac diseaseNorwood
Type
Original Article
Information
Cardiology in the Young , Volume 21 , Issue S2: A Holistic Approach to Hypoplastic Left Heart Syndrome and other evolving challenges in Pediatric and Congenital Cardiac Disease , 13 December 2011 , pp. 38 - 46
Copyright
Copyright © Cambridge University Press 2011

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