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Chapter 7.1 - Reversible Cerebral Vasoconstriction Syndrome

from 7 - Vasospastic Conditions and Other Vasculopathies

Published online by Cambridge University Press:  06 October 2022

Anita Arsovska
Affiliation:
University of Ss Cyril and Methodius
Derya Uluduz
Affiliation:
Istanbul Üniversitesi
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Summary

RCVS is a clinical radiological syndrome that typically presents with severe headache, with or without other neurological symptoms, and is associated with diffuse multifocal cerebral vasoconstriction that resolves spontaneously within 3 months. Most of the RCVS cases are associated with vasoactive medications, recreational drugs, pregnancy and postpartum state and migraine headaches.It usually begins with an acute, extremely severe thunderclap headache, like a headache in subarachnoid hemorrhage. Epileptic seizures have been reported and focal neurological deficit may present as a TIA or with visual disturbances. In more than 90% of patients, complete withdrawal of symptoms occur, but RCVS may be complicated with cerebral infarction, intracerebral hemorrhage, subarachnoid hemorrhage, or posterior reversible encephalopathy syndrome.Rarely, these complications lead to death. Catheter angiography, MR angiography or CT angiography may disclose a “string-of-beads” and “sausage and strings” appearance of vessels. In the treatment of cerebral vasospasm, the use of calcium channel blockers for about 4-8 weeks may be considered

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Chapter
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Rare Causes of Stroke
A Handbook
, pp. 293 - 298
Publisher: Cambridge University Press
Print publication year: 2022

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References

Ducros, A. Reversible cerebral vasoconstriction syndrome. Lancet Neurol. 2012;11: 906917.CrossRefGoogle ScholarPubMed
Cappelen-Smith, C, Calic, Z, Cordato, D. Reversible cerebral vasoconstriction syndrome: Recognition and treatment. Curr Treat Options Neurol. 2017;19: 21.CrossRefGoogle ScholarPubMed
Call, GK, Fleming, MC, Sealfon, S, et al. Reversible cerebral segmental vasoconstriction. Stroke. 1988;19: 11591170.CrossRefGoogle ScholarPubMed
Levitt, A, Zampolin, R, Burns, J, Bello, JA, Slasky, SE. Posterior reversible encephalopathy syndrome and reversible cerebral vasoconstriction syndrome: Distinct clinical entities with overlapping pathophysiology. Radiol Clin N Am. 2019;57: 11331146.CrossRefGoogle ScholarPubMed
Calabrese, LH, Dodick, DW, Schwedt, TJ, Singhal, AB. Narrative review: Reversible cerebral vasoconstriction syndromes. Ann Intern Med. 2007;146: 3444.CrossRefGoogle ScholarPubMed
Pilato, F, Distefano, M, Calandrelli, R. Posterior reversible encephalopathy syndrome and reversible cerebral vasoconstriction syndrome: Clinical and radiological considerations. Front Neurol. 2020;11: 34.Google Scholar
Chen, SP, Fuh, JL, Wang, SJ. Reversible cerebral vasoconstriction syndrome: Current and future perspectives. Expert Rev Neurother. 2011;11: 12651276.CrossRefGoogle ScholarPubMed
Miller, TR, Shivashankar, R, Mossa-Basha, M, Gandhi, D. Reversible cerebral vasoconstriction syndrome, part 1: Epidemiology, pathogenesis, and clinical course. Am J Neuroradiol. 2015;36: 13921399.CrossRefGoogle ScholarPubMed
Velez, A, McKinney, JS. Reversible cerebral vasoconstriction syndrome: A review of recent research. Curr Neurol Neurosci Rep. 2013;13: 319.CrossRefGoogle ScholarPubMed
Miller, TR, Shivashankar, R, Mossa-Basha, M, Gandhi, D. Reversible cerebral vasoconstriction syndrome, part 2: Diagnostic work-up, imaging evaluation, and differential diagnosis. Am J Neuroradiol. 2015;36: 15801588.CrossRefGoogle ScholarPubMed
Rocha, EA, Topcuoglu, MA, Silva, GS, Singhal, AB. RCVS2 score and diagnostic approach for reversible cerebral vasoconstriction syndrome. Neurology. 2019;92: e639e647.CrossRefGoogle ScholarPubMed

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