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Chapter 8.1 - Moyamoya Disease

from 8 - Other Non-inflammatory Vasculopathies

Published online by Cambridge University Press:  06 October 2022

Anita Arsovska
By
Bojana Žvan  and
Marjan Zaletel
Edited by
Derya Uluduz
Anita Arsovska
Affiliation:
University of Ss Cyril and Methodius
Derya Uluduz
Affiliation:
Istanbul Üniversitesi
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Summary

Moyamoya disease (MMD) is a cerebrovascular disorder characterised by progressive stenosis of the terminal portion of the internal carotid artery (ICA). The perforating arteries in the basal ganglia and thalamus markedly dilate and serve as an important collateral circulation, known as “Moyamoya” vessels. The clinical presentations of MMD include TIA, ischemic strokes, haemorrhagic strokes, seizures, headaches, and cognitive impairments. We present a 26-year old female patient that was examined due to headaches. For eight months, she had been admitted daily into the emergency hospital due to acute, unbearable headaches, which woke her up from her sleep. The MRI showed abnormalities suspicious for Moyamoya disease, which were confirmed with angiography

Keywords

Moyamoya diseasestrokeseizuresheadachecognitive impairmentangiography
Type
Chapter
Information
Rare Causes of Stroke
A Handbook
 , pp. 309 - 313
Publisher: Cambridge University Press
Print publication year: 2022

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References

Kuroda, S, Houkin, K. Moyamoya disease: Current concepts and future perspectives. Lancet Neurol. 2008;7(11): 1056–1066.CrossRefGoogle ScholarPubMed
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Scott, RM, Smith, ER. Moyamoya disease and moyamoya syndrome. N Engl J Med. 2009;360(12): 1226–1237.CrossRefGoogle ScholarPubMed
Research Committee on the Pathology and Treatment of Spontaneous Occlusion of the Circle of Willis: Health Labour Sciences Research Grant for Research on Measures for Intractable Diseases. Guidelines for diagnosis and treatment of moyamoya disease (spontaneous occlusion of the circle of Willis). Neurol Med Chir (Tokyo). 2012;52(5): 245–266.CrossRefGoogle Scholar
Bang, OY, Fujimura, M, Kim, SK. The pathophysiology of moyamoya disease: An update. J Stroke. 2016;18(1): 12–20.CrossRefGoogle ScholarPubMed

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