Book contents
- International Compendium of Movement Disorders
- International Compendium of Movement Disorders
- Copyright page
- Contents
- Contributors
- International Compendium of Movement Disorders
- Hypo- and Hyperkinetic, Dyscoordinative and Otherwise Inappropriate Motor and Behavioral Movement Disorders
- Section 1: Basic Introduction
- Section 2: Hypokinetic Movement Disorders
- Section 3: Hyperkinetic Movement Disorders
- Section 4: Dyscoordinative and Otherwise Inappropriate Motor Behaviors
- Chapter 46 Ataxia
- Chapter 47 Treatable Hereditary Cerebellar Ataxias
- Chapter 48 Gait and Balance Disorders
- Chapter 49 Episodic/Paroxysmal Movement Disorders
- Chapter 50 Sleep-Related Movement Disorders and Disturbances of Motor Control
- Chapter 51 Drug-Induced Movement Disorders
- Chapter 52 Psychiatric Movement Disorders
- Chapter 53 Functional Movement Disorders
- Section 5: Objectifying Movement Disorders
- Movement Disorders in Vivo: Video Fragments
- Acronyms and Abbreviations
- Index
- References
Chapter 49 - Episodic/Paroxysmal Movement Disorders
from Section 4: - Dyscoordinative and Otherwise Inappropriate Motor Behaviors
Published online by Cambridge University Press: 07 January 2025
By
Book contents
- International Compendium of Movement Disorders
- International Compendium of Movement Disorders
- Copyright page
- Contents
- Contributors
- International Compendium of Movement Disorders
- Hypo- and Hyperkinetic, Dyscoordinative and Otherwise Inappropriate Motor and Behavioral Movement Disorders
- Section 1: Basic Introduction
- Section 2: Hypokinetic Movement Disorders
- Section 3: Hyperkinetic Movement Disorders
- Section 4: Dyscoordinative and Otherwise Inappropriate Motor Behaviors
- Chapter 46 Ataxia
- Chapter 47 Treatable Hereditary Cerebellar Ataxias
- Chapter 48 Gait and Balance Disorders
- Chapter 49 Episodic/Paroxysmal Movement Disorders
- Chapter 50 Sleep-Related Movement Disorders and Disturbances of Motor Control
- Chapter 51 Drug-Induced Movement Disorders
- Chapter 52 Psychiatric Movement Disorders
- Chapter 53 Functional Movement Disorders
- Section 5: Objectifying Movement Disorders
- Movement Disorders in Vivo: Video Fragments
- Acronyms and Abbreviations
- Index
- References
Summary
Paroxysmal movement disorders are a heterogeneous group of syndromes that produce recurrent attacks of involuntary movements without loss of consciousness as their common feature. In this chapter a very short historical overview is given before discussing the current classification and diagnostic criteria of the three main types of paroxysmal movement disorders: paroxysmal kinesigenic dyskinesia, paroxysmal non-kinesigenic dyskinesia and paroxysmal exercise–induced dyskinesia. During the past two decades, a rapidly growing number of genes that cause paroxysmal movement disorders have been reported. This also challenges the current classification because many genetic forms of paroxysmal dyskinesia can be caused by mutations of the same gene. Nevertheless, a first clinical description and classification appears to be reasonable and important. The chapter also describes the episodic ataxias, along with their genetic background, as well as the non-genetic causes of paroxysmal movement disorders, which include vascular, structural, infectious, inflammatory and metabolic causes. The last part of the chapter deals with a proposed approach to a patient with paroxysmal dyskinesia in daily practice.
Keywords
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- Information
- International Compendium of Movement Disorders , pp. 617 - 627Publisher: Cambridge University PressPrint publication year: 2025
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