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Chapter 43 - Chorea

from Section 3: - Hyperkinetic Movement Disorders

Published online by Cambridge University Press:  07 January 2025

By
Jan Roth
Edited by
Erik Ch. Wolters  and
Christian R. Baumann
Erik Ch. Wolters
Affiliation:
Universität Zürich
Christian R. Baumann
Affiliation:
Universität Zürich
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Summary

Chorea is a state of excessive, spontaneous movements, irregularly timed, non-repetitive, randomly distributed, and abrupt in character. The severity of movements may vary from restlessness with mild intermittent exaggeration of gesture and expression, fidgeting movements of the hands, and dance-like gait to a continuous flow of disabling violent movements. The pathogenesis of chorea is mainly related to striatal dysfunction. The classification of the causes of choreatic dyskinesias is complex and involves many clinical entities, both hereditary and acquired. The severity of chorea can be reduced by antipsychotics, tetrabenazine or benzodiazepines.

Keywords

ChoreaHuntington disease (HD)Friedreich’s ataxiaWilson’s diseaseataxia–telangiectasiaSydenham’s chorealupus erythematosusantiphospholipid syndrome
Type
Chapter
Information
International Compendium of Movement Disorders , pp. 540 - 556
Publisher: Cambridge University Press
Print publication year: 2025

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  • Chorea
  • Edited by Erik Ch. Wolters, Universität Zürich, Christian R. Baumann, Universität Zürich
  • Book: International Compendium of Movement Disorders
  • Online publication: 07 January 2025
  • Chapter DOI: https://doi.org/10.1017/9781108989855.045
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  • Chorea
  • Edited by Erik Ch. Wolters, Universität Zürich, Christian R. Baumann, Universität Zürich
  • Book: International Compendium of Movement Disorders
  • Online publication: 07 January 2025
  • Chapter DOI: https://doi.org/10.1017/9781108989855.045
Available formats
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Save book to Google Drive

To save content items to your account, please confirm that you agree to abide by our usage policies. If this is the first time you use this feature, you will be asked to authorise Cambridge Core to connect with your account. Find out more about saving content to Google Drive.

  • Chorea
  • Edited by Erik Ch. Wolters, Universität Zürich, Christian R. Baumann, Universität Zürich
  • Book: International Compendium of Movement Disorders
  • Online publication: 07 January 2025
  • Chapter DOI: https://doi.org/10.1017/9781108989855.045
Available formats
×