Book contents
- Congenital Cardiac Anesthesia
- Congenital Cardiac Anesthesia
- Copyright page
- Dedication
- Contents
- Contributors
- Introduction
- Chapter 1 A Congenital Heart Disease Primer
- Section 1 Left-to-Right Shunts
- Section 2 Right-Sided Obstructive Lesions
- Section 3 Left-Sided Obstructive Lesions
- Section 4 Complex Mixing Lesions
- Section 5 Single-Ventricle Physiology
- Section 6 Heart Failure, Mechanical Circulatory Support, and Transplantation
- Section 7 Miscellaneous Lesions and Syndromes
- Chapter 40 Idiopathic Pulmonary Hypertension
- Chapter 41 Pulmonary Hypertension and Congenital Heart Disease
- Chapter 42 Pulmonary Hypertension and Prematurity
- Chapter 43 Pulmonary Hypertension and Moyamoya Disease
- Chapter 44 Vascular Ring
- Chapter 45 Pericardial Effusion
- Chapter 46 Kawasaki Disease
- Chapter 47 VACTERL Syndrome
- Chapter 48 Hurler Syndrome
- Chapter 49 Long QT Syndrome
- Chapter 50 Marfan Syndrome
- Index
- References
Chapter 41 - Pulmonary Hypertension and Congenital Heart Disease
from Section 7 - Miscellaneous Lesions and Syndromes
Published online by Cambridge University Press: 09 September 2021
Book contents
- Congenital Cardiac Anesthesia
- Congenital Cardiac Anesthesia
- Copyright page
- Dedication
- Contents
- Contributors
- Introduction
- Chapter 1 A Congenital Heart Disease Primer
- Section 1 Left-to-Right Shunts
- Section 2 Right-Sided Obstructive Lesions
- Section 3 Left-Sided Obstructive Lesions
- Section 4 Complex Mixing Lesions
- Section 5 Single-Ventricle Physiology
- Section 6 Heart Failure, Mechanical Circulatory Support, and Transplantation
- Section 7 Miscellaneous Lesions and Syndromes
- Chapter 40 Idiopathic Pulmonary Hypertension
- Chapter 41 Pulmonary Hypertension and Congenital Heart Disease
- Chapter 42 Pulmonary Hypertension and Prematurity
- Chapter 43 Pulmonary Hypertension and Moyamoya Disease
- Chapter 44 Vascular Ring
- Chapter 45 Pericardial Effusion
- Chapter 46 Kawasaki Disease
- Chapter 47 VACTERL Syndrome
- Chapter 48 Hurler Syndrome
- Chapter 49 Long QT Syndrome
- Chapter 50 Marfan Syndrome
- Index
- References
Summary
The risk of perioperative morbidity and mortality is increased in patients with pulmonary hypertension regardless of the procedure. This is particularly true for patients with multifactorial pulmonary hypertension. We present such a patient here with a history of Down syndrome and repaired congenital heart disease who is scheduled to undergo an elective tympanoplasty. Anesthetic issues relevant to the care of a patient with Down syndrome, atrioventricular septal defect, and pulmonary hypertension are discussed, with a focus on assessment and intraoperative planning.
Keywords
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- Information
- Congenital Cardiac AnesthesiaA Case-based Approach, pp. 314 - 322Publisher: Cambridge University PressPrint publication year: 2021
References
Suggested Reading
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Bush, D., Galambos, C., Ivy, D. D., et al. Clinical characteristics and risk factors for developing pulmonary hypertension in children with Down syndrome. J Pediatr 2018; 202: 212–19.CrossRefGoogle ScholarPubMed
Hansmann, G. and Apitz, C. Treatment of children with pulmonary hypertension. Expert consensus statement on the diagnosis and treatment of pediatric pulmonary hypertension. The European Paediatric Pulmonary Vascular Disease Network, endorsed by ISHLT and DGPK. Heart 2016; 102: ii67–ii85.Google ScholarPubMed
Shukla, A. C. and Almodovar, M. C. Anesthesia considerations for children with pulmonary hypertension. Pediatr Crit Care Med 2010; 11: S7–73.CrossRefGoogle ScholarPubMed
Twite, M. D. and Friesen, R. H. The anesthetic management of children with pulmonary hypertension in the cardiac catheterization laboratory. Anesthesiol Clin 2014; 23: 157–73.Google Scholar