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Two Cases of the Sturge-Weber Syndrome

Published online by Cambridge University Press:  29 January 2018

Ranan Rimon  and
Olavi Katila
Ranan Rimon
Affiliation:
University Psychiatric Clinic, Kupittaan Sairaala, Turku Hesperia Hospital, Helsinki, Finland
Olavi Katila
Affiliation:
Neurological Department, Hesperia Hospital, Helsinki, Finland
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Extract

The Sturge-Weber syndrome belongs to the relatively uncommon group of ailments known as heredodegenerative disorders. In 1879 Sturge described a case of epilepsy in a young girl who exhibited a congenital glaucoma and a facial angioma or naevus flammeus. Sturge speculated that the patient's convulsions were caused by a similar naevus formation in the brain. Kalischer (1897, 1901) discovered angiomatotic changes in the meninges, and later the typical calcium deposits corresponding to these angio-mata were found in X-ray examinations by Weber (1922), Dimitri (1923), and Krabbe (1934). The appellation of the Sturge-Weber syndrome varies, owing to the number of its investigators. Levison (1953) calls attention to this question of nomenclature.

Type
Research Article
Information
The British Journal of Psychiatry , Volume 112 , Issue 488 , July 1966 , pp. 709 - 711
Copyright
Copyright © Royal College of Psychiatrists, 1966 

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References

Dimitri, V. (1923). “Tumor cerebral congenito (angioma cavernosa)”. Rev. Asoc. med. argent., 36, 63, cited by Levison.Google Scholar
Greenwald, H. M. and Koota, J. (1936). “Associated facial and intracranial hemangiomas”. Amer. J. Dis. Child., 51, 445.Google Scholar
Kalischer, S. (1897). “Demonstration des Gehirns eines Kindes mit Teleangiectasie der linksseitigen Gesichtskopfhaut und Hirnoberfläche”. Berl. klin. Wchnschr., 34, 1059.Google Scholar
Kalischer, S. (1901). “Ein Fall von Teleangiectasie (Angiom) des Gesichts und der weichen Hirnhaut”. Arch. f. Psychiatr., 34, 171.Google Scholar
Krabbe, K. H. (1934). “Facial and meningeal angiomatosis associated with calcification of the brain cortex”. Arch. Neurol. Psychiat., 32, 737.Google Scholar
Levison, H. (1953). “Remarks on the Sturge-Kalischer-Weber-Dimitri-Krabbe disease”. Acta psychiat. neurol. scand., 30, 257.Google Scholar
Morrice, J. W. K. and Small, W. M. (1963). “A case of Sturge-Weber syndrome”. Brit. J. Psychiat., 109, 211.Google Scholar
Peterman, A. F. Hayles, A. B. Dockerty, M. B. and Love, J. S. (1958). “Encephalotrigeminal angiomatosis (Sturge-Weber disease). Clinical study of thirty-five cases”. J.A.M.A., 167, 2169.CrossRefGoogle Scholar
Sheidina, R. B. (1960). “Clinical aspects of Sturge-Weber disease in children”. J. Nevropat. Psichiat., 60, 836.Google Scholar
Sturge, W. A. (1879). “Case of partial epilepsy, apparently due to lesion of one of vasomotor centres of brain”. Tr. clin. Soc. London, 12, 162.Google Scholar
Weber, F. P. (1922). “Right-sided hemi-hypodystrophy resulting from right-sided congenital spastic hemiplegia with morbid condition of left side of brain revealed by radiograms”. J. Neurol. Psychopat., 3, 134.Google Scholar
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