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Unilateral hearing loss as primary symptom of craniopharyngioma in a six-year-old girl

Published online by Cambridge University Press:  05 February 2008

R Hofman  and
H J Rosingh
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Abstract

Objective:

We report a rare case of otological presentation of craniopharyngioma.

Method:

Case report and review of world literature concerning presentations of craniopharyngioma.

Results:

A six-year-old girl was referred to our department with unilateral hearing loss. This appeared to be a complete sensorineural hearing loss. Otoacoustic emissions were reproducible on both sides. Magnetic resonance scanning revealed a massive, cystic craniopharyngioma exerting pressure on the patient's ventricular system and brainstem and also invading the internal acoustic canal. The mass was resected via a craniotomy. The patient's hearing loss completely recovered, and she experienced no neurological or endocrinological side effects of the treatment. Craniopharyngioma have a prevalence of 0.13–2:100 000.

Conclusion:

Craniopharyngioma is a rare disease. First presentation with otological symptoms is extremely rare. Otoacoustic emissions can differentiate between cochlear and retrocochlear causes of sensorineural hearing loss.

Keywords

Hearing LossCraniopharyngiomaOtoacoustic Emissions
Type
Research Article
Information
The Journal of Laryngology & Otology , Volume 122 , Issue 3 , March 2008 , e10
Copyright
Copyright © JLO (1984) Limited 2008

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