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Simultaneous bilateral cochlear implantation in a five-month-old child with Usher syndrome

Published online by Cambridge University Press:  16 July 2015

A A Alsanosi
A A Alsanosi*
Affiliation:
Department of Otolaryngology, King Saud University, Riyadh, Kingdom of Saudi Arabia
*
Address for correspondence: Dr Abdulrahman Alsanosi, Department of Otolaryngology and Head and Neck Surgery, King Saud University, PO Box 245, Riyadh 11411, Kingdom of Saudi Arabia Fax: 00966 1 4775748 E-mail: [email protected]
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Abstract

Objective:

To report a rare case of simultaneous bilateral cochlear implantation in a five-month-old child with Usher syndrome.

Method:

Case report.

Results:

A five-month-old boy with Usher syndrome and congenital profound bilateral deafness underwent simultaneous bilateral cochlear implantation. The decision to perform implantation in such a young child was based on his having a supportive family and the desire to foster his audiological development before his vision deteriorated. The subject experienced easily resolvable intra- and post-operative adverse events, and was first fitted with an externally worn audio processor four weeks after implantation. At 14 months of age, his audiological development was age-appropriate.

Conclusion:

Simultaneous bilateral cochlear implantation is possible, and even advisable, in children as young as five months old when performed by an experienced implantation team.

Keywords

HematomaBone MarrowUsher SyndromeHearing LossCochlear Implantation
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 129 , Issue 9 , September 2015 , pp. 919 - 922
Copyright
Copyright © JLO (1984) Limited 2015 

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