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The Scheibe cochlea deformity with macrocephaly: a case for single channal implantation

Published online by Cambridge University Press:  29 June 2007

J. Ray ,
R. F. Gay ,
Z. H. Vanat  and
J. A. Begg
J. Ray*
Affiliation:
East of England Cochlear Implant Programme, Addenbrooke's Hospital, Cambridge, UK
R. F. Gay
Affiliation:
East of England Cochlear Implant Programme, Addenbrooke's Hospital, Cambridge, UK
Z. H. Vanat
Affiliation:
East of England Cochlear Implant Programme, Addenbrooke's Hospital, Cambridge, UK
J. A. Begg
Affiliation:
East of England Cochlear Implant Programme, Addenbrooke's Hospital, Cambridge, UK
*
Address for correspondence: Mr J. Ray, M.S., F.R.C.S., 89 Longfleet Road, Poole BH15 2HP
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Abstract

An 11-year-old congenitally deaf child with bilateral primitive common cavity (Scheibe type) cochleosaccular dysplasia and benign familial macrocephaly was implanted with an extracochlear single channel device with an ear level speech processor. This paper describes the assessment, findings, dilemmas in decision making, surgical procedure and the favourable outcome after implanting. The relevant literature has been reviewed and our case is presented for the unusual combination of features.

Keywords

Cochiear implantCochleaAbnonnalitiesDeafness, congenital
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 112 , Issue 11 , November 1998 , pp. 1065 - 1068
Copyright
Copyright © JLO (1984) Limited 1998

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