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Hyperacusis and Williams syndrome

Published online by Cambridge University Press:  29 June 2007

Ajay Nigam
Affiliation:
Department of Otolaryngology, Royal Infirmary, Sunderland.
Peter R. Samuel*
Affiliation:
Department of Otolaryngology, Royal Infirmary, Sunderland.
*
Mr P.R. Samuel, F.R.C.S.E., Dalkeith Lodge, Aykley Heads Farm, Durham DH1 5AN.

Abstract

Abnormal sensitivity to environmental sounds is a short-term feature often observed following insertion of grommets. Here we describe a child with this symptom who was found to have Williams syndrome, a condition in which hyperacusis is observed in 95 per cent of patients.

Type
Clinical Records
Copyright
Copyright © JLO (1984) Limited 1994

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