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Failure to control the airway in a patient with Hunter's syndrome

Published online by Cambridge University Press:  29 June 2007

Luis Gaitini ,
Milo Fradis ,
Sonia Vaida ,
Geoffrey Collins ,
Millian Croitoru ,
Mustafa Somri ,
Zvi Borochovltz  and
Avishai Golz
Luis Gaitini
Affiliation:
Departments of Anaesthesiology and Otolaryngology – Head and Neck Surgery, Bnai Zion Medical Center, Rambam Medical Center and The Bruce Rappaport Faculty of Medicine, Technion-Israel Institute of Technology, Haifa, Israel.
Milo Fradis*
Affiliation:
Departments of Anaesthesiology and Otolaryngology – Head and Neck Surgery, Bnai Zion Medical Center, Rambam Medical Center and The Bruce Rappaport Faculty of Medicine, Technion-Israel Institute of Technology, Haifa, Israel.
Sonia Vaida
Affiliation:
Departments of Anaesthesiology and Otolaryngology – Head and Neck Surgery, Bnai Zion Medical Center, Rambam Medical Center and The Bruce Rappaport Faculty of Medicine, Technion-Israel Institute of Technology, Haifa, Israel.
Geoffrey Collins
Affiliation:
Departments of Anaesthesiology and Otolaryngology – Head and Neck Surgery, Bnai Zion Medical Center, Rambam Medical Center and The Bruce Rappaport Faculty of Medicine, Technion-Israel Institute of Technology, Haifa, Israel.
Millian Croitoru
Affiliation:
Departments of Anaesthesiology and Otolaryngology – Head and Neck Surgery, Bnai Zion Medical Center, Rambam Medical Center and The Bruce Rappaport Faculty of Medicine, Technion-Israel Institute of Technology, Haifa, Israel.
Mustafa Somri
Affiliation:
Departments of Anaesthesiology and Otolaryngology – Head and Neck Surgery, Bnai Zion Medical Center, Rambam Medical Center and The Bruce Rappaport Faculty of Medicine, Technion-Israel Institute of Technology, Haifa, Israel.
Zvi Borochovltz
Affiliation:
Departments of Anaesthesiology and Otolaryngology – Head and Neck Surgery, Bnai Zion Medical Center, Rambam Medical Center and The Bruce Rappaport Faculty of Medicine, Technion-Israel Institute of Technology, Haifa, Israel.
Avishai Golz
Affiliation:
Departments of Anaesthesiology and Otolaryngology – Head and Neck Surgery, Bnai Zion Medical Center, Rambam Medical Center and The Bruce Rappaport Faculty of Medicine, Technion-Israel Institute of Technology, Haifa, Israel.
*
Address for correspondence: Milo Fradis, M.D., Department of Otolaryngology – Head and Neck Surgery, Bnai Zion Medical Center, P.O.B. 4940, 31048 Haifa, Israel.
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Abstract

Hunter's syndrome is due to recessively inherited mucopolysaccharide storage diseases. The anaesthetic complications in this syndrome are related to the organs involved in the disease, but pertain especially to upper airway obstruction problems. We report a patient with Hunter's syndrome who, while under general anaesthesia for a simple procedure (the introduction of bilateral grommets), suffered a fatal outcome.

Keywords

Mucopolysaccharidosis IIAnaesthesiageneral
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 112 , Issue 4 , April 1998 , pp. 380 - 382
Copyright
Copyright © JLO (1984) Limited 1998

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