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Cochlear implantation is a therapeutic option for superficial siderosis patients with sensorineural hearing loss

Published online by Cambridge University Press:  09 February 2016

R Omichi ,
S Kariya ,
Y Maeda  and
K Nishizaki
R Omichi
Affiliation:
Department of Otolaryngology – Head and Neck Surgery, Graduate School of Medicine, Dentistry and Pharmaceutical Sciences, Okayama University, Japan
S Kariya*
Affiliation:
Department of Otolaryngology – Head and Neck Surgery, Graduate School of Medicine, Dentistry and Pharmaceutical Sciences, Okayama University, Japan
Y Maeda
Affiliation:
Department of Otolaryngology – Head and Neck Surgery, Graduate School of Medicine, Dentistry and Pharmaceutical Sciences, Okayama University, Japan
K Nishizaki
Affiliation:
Department of Otolaryngology – Head and Neck Surgery, Graduate School of Medicine, Dentistry and Pharmaceutical Sciences, Okayama University, Japan
*
Address for correspondence: Dr Shin Kariya, Department of Otolaryngology – Head and Neck Surgery, Graduate School of Medicine, Dentistry and Pharmaceutical Sciences, Okayama University, 2-5-1 Shikata-Cho, Kita-Ku, Okayama 700-8558, Japan Fax: 81 86 235 7308 E-mail: [email protected]
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Abstract

Background:

Superficial siderosis is a rare disease that results from chronic bleeding in the subarachnoid space. Haemosiderin deposits throughout the subpial layers of the brain and spinal cord lead to progressive sensorineural hearing loss, which is seen in 95 per cent of patients with superficial siderosis. The impact of cochlear implantation on the quality of life of superficial siderosis patients is under debate.

Case report:

A 38-year-old male with superficial siderosis presented with bilateral progressive sensorineural hearing loss. The patient underwent cochlear implantation and his quality of life was improved as evaluated by the Abbreviated Profile of Hearing Aid Benefit inventory.

Conclusion:

The remarkable improvement in Abbreviated Profile of Hearing Aid Benefit scores shown in this study indicates that cochlear implantation leads to a better quality of life in superficial siderosis patients.

Keywords

SiderosisHearing LossCochlear ImplantationsQuality Of LifeQuestionnaires
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 130 , Issue 4 , April 2016 , pp. 408 - 411
Copyright
Copyright © JLO (1984) Limited 2016 

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