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Cochlear implantation in superficial siderosis

Published online by Cambridge University Press:  29 June 2007

Richard M. Irving  and
John M. Graham
Richard M. Irving*
Affiliation:
Ferens Cochlear Implant Centre, The Royal Ear Hospital, London, UK.
John M. Graham
Affiliation:
Ferens Cochlear Implant Centre, The Royal Ear Hospital, London, UK.
*
Address for correspondence: Mr Richard M. Irving, M.D., F.R.C.S., Deparment of Otolaryngology – Head and Neck Surgery, University of California, San Francisco, 350 Parnassus Avenue, Suite 210, San Francisco, California 94117, U.S.A. Fax: 00 1 415 476 0666
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Abstract

Superficial siderosis is a rare central nervous system disorder characterized by deafness, ataxia, and pyramidal signs. The hearing loss is believed to be predominantly neural and is usuallly progressive and bilateral. Careful assessment is therefore necessary to determine the best approach to hearing rehabilitation. A case is presented of usperficial siderosis in a young woman who has benegited significantly from cochlear implantation using the Nucleus dvice.

Keywords

SiderosisHearing loss, sensorineuralCochlear implant
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 110 , Issue 12 , December 1996 , pp. 1151 - 1153
Copyright
Copyright © JLO (1984) Limited 1996

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Footnotes

Presented at IIIrd Paris International Congress on Cochlear Implants April, 1995

References

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