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Von Hippel-Lindau disease associated with an invasive choroid plexus tumour presenting as a middle ear mass

Published online by Cambridge University Press:  29 June 2007

T. L. Blamires ,
I. Friedmann  and
D. A. Moffat
T. L. Blamires*
Affiliation:
Departments of Ophthalmology, Addenbrooke's Hospital, Cambridge.
I. Friedmann
Affiliation:
Department of Pathology, North wick Park Hospital, Middlesex.
D. A. Moffat
Affiliation:
Department of Otoneurosurgery, Addenbrooke's Hospital, Cambridge.
*
Mrs Trudi Blamires, F.R.C.S., 4 Hinton Avenue, Cambridge, CB1 4AS.
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Abstract

Cerebellar haemangioblastomata and angiomata of the retina are the most common vascular tumours seen in von Hippel-Lindau disease. A definite association between this condition and choroid plexus tumour has not been described previously and its presentation as a middle ear mass is unique.

Keywords

EarmiddleVon Hippel-Lindau disease
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 106 , Issue 5 , May 1992 , pp. 429 - 435
Copyright
Copyright © JLO (1984) Limited 1992

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