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Successful bone-anchored hearing aid implantation in a patient with osteogenesis imperfecta

Published online by Cambridge University Press:  24 September 2015

M B Coutinho ,
C Marques ,
G J Mendes  and
C Gonçalves
M B Coutinho*
Affiliation:
Otolaryngology Department, Lusíadas Hospital, Porto, Portugal
C Marques
Affiliation:
Faculty of Medicine, Girona University, Spain
G J Mendes
Affiliation:
Otolaryngology Department, Porto Hospital Center, Portugal
C Gonçalves
Affiliation:
Widex Hearing Center, Lisbon, Portugal
*
Address for correspondence: Dr Miguel Bebiano Coutinho, Otolaryngology Department, Hospital Lusíadas Porto, Unidade de Otorrinolaringologia, Avenida da Boavista, 171, 4050-115 Porto, Portugal E-mail: [email protected]
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Abstract

Objective:

To report a case of successful bone-anchored hearing aid implantation in an adult patient with type III osteogenesis imperfecta, which is commonly regarded as a contraindication to this procedure.

Case report:

A 45-year-old man with type III osteogenesis imperfecta presented with mixed hearing loss. There was a mild sensorineural component in both ears, with an air–bone gap between 45 and 50 dB HL. He was implanted with a bone-anchored hearing aid. The audiological outcome was good, with no complications and good implant stability (as measured by resonance frequency analysis).

Conclusion:

To our knowledge, this is the first recorded case of bone-anchored hearing aid implantation in a patient with osteogenesis imperfecta.

Keywords

Osteogenesis ImperfectaHearing LossOsseointegrationHearing Aids
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 129 , Issue 11 , November 2015 , pp. 1133 - 1136
Copyright
Copyright © JLO (1984) Limited 2015 

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