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Large endolymphatic sac. A congenital deformity of the inner ear shown by magnetic resonance imaging

Published online by Cambridge University Press:  29 June 2007

P. D. Phelps ,
C. F. O. Mahoney  and
L. M. Luxon
P. D. Phelps*
Affiliation:
Department of Radiology, Royal National Throat, Nose and Ear HospitalLondon, UK.
C. F. O. Mahoney
Affiliation:
Department of Audiological Medicine. Great Ormond Street Hospital for ChildrenLondon, UK.
L. M. Luxon
Affiliation:
Institute of Laryngology and Otology, London, UK.
*
Address for correspondence: Dr P. D. Phelps, M.D., F.R.C.S., F.R.C.R., D.M.R.D., Consultant Radiologist, The Royal National Throat, Nose and Ear Hospital, Gray's Inn Road, London WC1X 8DA.
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Abstract

Fluctuant and progressive hearing impairment in a patient with a wide vestibular aqueduct has been called the ‘large vestibular aqueduct syndrome’. Recently reports of magnetic resonance imaging (MRI) studies describe enlargement of the endolymphatic sac and duct in patients shown to have large vestibular aqueducts by computed tomography (CT). A patient with progressive deafness was shown to have borderline or slightly enlarged vestibular aqueducts by re-formatted sagittal CT. However, MRI in axial and sagittal planes gave a more satisfactory demonstration of both aqueduct and endolymphatic sac enlargement.

Keywords

Magnetic resonance imagingTomography, X-ray computedVestibular aqueduct
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 111 , Issue 8 , August 1997 , pp. 754 - 756
Copyright
Copyright © JLO (1984) Limited 1997

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