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Hearing loss in multiple sclerosis: localization of the auditory pathway lesion according to electrocochleographic findings

Published online by Cambridge University Press:  29 June 2007

N. Marangos
N. Marangos*
Affiliation:
HNO-Klinik, Albert-Ludwigs-Universität Freiburg, Germany.
*
Address for correspondence: Dr Med. N. Marangos, HNO-Klinik, Albert-Ludwigs-Universität Freiburg, Killianstr. 5, 79106 Freiburg, Germany.
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Abstract

Multiple sclerosis is known to affect the myelin of the auditory pathway resulting in acute hearing loss. Two cases of sudden deafness due to multiple sclerosis have been evaluated by conventional audiometry, brainstem auditory evoked response audiometry and transtympanic electrocochleography. The abnormalities of the compound action potential in both patients (enhanced latency, abnormal adaptation using fast stimulus rate) and the normal receptor potentials (cochlear microphonic, summating potential), as well as the absence of brainstem responses suggest a disturbance of synchronization at the level of the first auditory neurone. The electrocochleography provides valuable information for the topodiagnosis of this and other neural hearing losses, especially in the absence of reliable brainstem responses.

Keywords

Multiple sclerosisHearing loss, sensorineuralAudiometry, evoked response
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 110 , Issue 3 , March 1996 , pp. 252 - 257
Copyright
Copyright © JLO (1984) Limited 1996

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