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Familial paraganglioma

Published online by Cambridge University Press:  29 June 2007

S. M. Wharton  and
A. Davis
S. M. Wharton*
Affiliation:
Department of Otolaryngology, Head and Neck Surgery, Queen Alexandra Hospital, Cosham, Portsmouth, UK
A. Davis
Affiliation:
Department of Otolaryngology, Head and Neck Surgery, Queen Alexandra Hospital, Cosham, Portsmouth, UK
*
Address for correspondence: Dr S. M. Wharton, Department of Otorhinolaryngology, Head and Neck Surgery, Queen Alexandra Hospital, Cosham, Portsmouth, Hants.
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Abstract

Non-secreting paragangliomas are rare tumours usually present in the head and neck. We describe an unusual case of familial paraganglioma with cranial nerve palsies. After exhaustive investigation, a vagal paraganglioma was found and excised. The positive family history of paraganglioma was of significance, although this was only present in one of five generations. The diagnosis and management of non-secreting paragangliomas is discussed.

Keywords

ParagangliomaVagus nerveFamily
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 110 , Issue 7 , July 1996 , pp. 688 - 690
Copyright
Copyright © JLO (1984) Limited 1996

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