Hostname: page-component-cd9895bd7-q99xh Total loading time: 0 Render date: 2024-12-26T07:36:03.790Z Has data issue: false hasContentIssue false
  • English
  • Français

Congenital stapedial suprastructure fixation with normal footplate mobility: case report

Published online by Cambridge University Press:  14 October 2009

J H Lee ,
S H Jung ,
H C Kim ,
C H Park  and
S M Hong
J H Lee*
Affiliation:
Department of Otorhinolaryngology-Head and Neck Surgery, School of Medicine, Hallym University, Chuncheon, South Korea
S H Jung
Affiliation:
Department of Otorhinolaryngology-Head and Neck Surgery, Wonju College of Medicine, Yonsei University, Wonju, South Korea
H C Kim
Affiliation:
Department of Radiology, School of Medicine, Hallym University, Chuncheon, South Korea
C H Park
Affiliation:
Department of Otorhinolaryngology-Head and Neck Surgery, School of Medicine, Hallym University, Chuncheon, South Korea
S M Hong
Affiliation:
Department of Otorhinolaryngology-Head and Neck Surgery, School of Medicine, Hallym University, Chuncheon, South Korea
*
Address for correspondence: Dr J H Lee, Department of Otorhinolaryngology-Head and Neck Surgery, Chuncheon Sacred Heart Hospital, School of Medicine, Hallym University, #153 Kyo-Dong, Chuncheon, Kangwon, South Korea. Fax: 82 33 241 2909 E-mail: [email protected]
Get access Rights & Permissions [Opens in a new window]

Abstract

Objective:

We report a case of bilateral conductive hearing loss caused by stapedial suprastructure fixation with normal footplate mobility.

Case report:

A 50-year-old woman had suffered hearing loss in both ears since childhood. Exploratory tympanotomy revealed immobility of the stapes due to a bony bridge between the stapedial suprastructure and the fallopian canal. The incus was missing, while the malleus handle was minimally deformed. The mobility of the stapes footplate was normal. Post-operatively, the hearing in the right ear improved both subjectively and audiographically, while that in the left ear did not improve because of footplate subluxation during surgery.

Conclusion:

This is a rare case of congenital stapedial suprastructure fixation with normal footplate mobility. In this patient, development of the second branchial arch was arrested. When performing exploratory tympanotomy for stapedial fixation, one must keep in mind that normal footplate mobility is possible.

Keywords

Middle EarStapesConductive DeafnessCongenital
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 124 , Issue 6 , June 2010 , pp. 680 - 683
Copyright
Copyright © JLO (1984) Limited 2009

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1 Bailey, BJ. Head & Neck Surgery – Otolaryngology, 3rd edn. Philadelphia: Lippincott Williams & Wilkins, 2001;1612–14Google Scholar
2 Nomura, Y, Nagaro, Y, Fukaja, T. Anomalies of the middle ear. Laryngoscope 1988;98:390–3CrossRefGoogle ScholarPubMed
3 Charachon, R, Barthez, M, Lavieille, JP. Minor malformations of the ear ossicles. New classification and therapeutic results. Ann Otolaryngol Chir Cervicofac 1994;111:69–74Google ScholarPubMed
4 Teunissen, B, Cremers, WR. Classification of congenital middle ear abnormalies: report on 144 ears. Ann Otol Rhinol Laryngol 1993;102:606–12CrossRefGoogle Scholar
5 Henner, R, Buckingham, RA. The recognition and surgical treatment of congenital ossicular defects. Laryngoscope 1956;66:526–39CrossRefGoogle ScholarPubMed
6 Park, K, Moon, SK. Clinical evaluation of congenital stapes fixation. Korean J Otolaryngol 1994;38:537–43Google Scholar
7 Kinsellar, JB, Kerr, AG. Familial stapes superstructure fixation. J Laryngol Otol 1993;107:36–8CrossRefGoogle Scholar
8 Nandapalan, V, Tos, M. Isolated congenital stapes suprastructure fixation. J Laryngol Otol 1999;113:798–802CrossRefGoogle ScholarPubMed
9 Hough, JV. Malformations and anatomical variations seen in the middle ear during the operation for mobilization of the stapes. Laryngoscope 1958;68:1337–79CrossRefGoogle ScholarPubMed
10 Henner, R. Congenital middle ear malformations. Arch Otolaryngol 1960;71:454–8CrossRefGoogle ScholarPubMed
11 Gerhardt, HJ, Otto, HD. Stapedial malformation. Acta Otolaryngological 1970;70:35–44CrossRefGoogle Scholar
12 Ching, HY, Bottrill, ID. An unusual stapes. Surg Radiol Anat 2006;28:474–6CrossRefGoogle ScholarPubMed
13 Cressman, WR, Pensak, MI. Surgical aspects of congenital aural atresia. Otolaryngol Clin North Am 1994;27:621–32CrossRefGoogle ScholarPubMed