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Cochlear implants for congenital deformities

Published online by Cambridge University Press:  29 June 2007

P. D. Phelps*
Affiliation:
London
*
Consultant Radiologist, The Royal National Throat, Nose and Ear Hospital, Gray's Inn Road, London WCIX 8DA.

Abstract

There have been few accounts of multi-channel cochlear implants in patients with congenital structural deformities of the inner ear which are associated with severe and sometimes progressive deafness. These malformations can now be recognized easily on 2 plane thin section high resolution CT studies which are mandatory for the pre-implantation assessment. However, no attempt seems to have been made to describe which of these malformations would be suitable for an implant or for which would this procedure be contra-indicated. True Mondini deformity of both the cochlea and dilated vestibular aqueduct type would appear suitable for a multi channel implant, but this type of implant should not be used for a primitive otocyst, severe labyrinthine dysplasia or the characteristic X-linked deformity.

Type
Main Articles
Copyright
Copyright © JLO (1984) Limited 1992

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