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Bilateral narrow duplication of the internal auditory canal

Published online by Cambridge University Press:  29 April 2010

L O M Coelho ,
S E Ono ,
A Carvalho Neto ,
J F Polanski  and
M Buschle
L O M Coelho
Affiliation:
Department of Radiology, DAPI-Diagnóstico Avançado por Imagem, Curitiba, PR Brazil
S E Ono*
Affiliation:
Department of Radiology, DAPI-Diagnóstico Avançado por Imagem, Curitiba, PR Brazil
A Carvalho Neto
Affiliation:
Department of Radiology, DAPI-Diagnóstico Avançado por Imagem, Curitiba, PR Brazil
J F Polanski
Affiliation:
Department of Otorhinolaryngology, Hospital Iguaçu, Curitiba, PR Brazil
M Buschle
Affiliation:
Department of Otorhinolaryngology, Hospital Iguaçu, Curitiba, PR Brazil
*
Address for correspondence: Dr Sergio E Ono, Clínica DAPI, Rua Brigadeiro Franco, 122 CEP 80430-210, Curitiba, PR Brazil. E-mail: [email protected]
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Abstract

Aim:

To demonstrate diagnostic imaging of an extremely rare presentation of bilateral narrow duplication of the internal auditory canal.

Case report:

An adolescent boy with profound sensorineural hearing loss presented for hearing rehabilitation. Imaging studies (i.e. multidetector computed tomography and magnetic resonance imaging) clearly demonstrated bilateral duplication of the internal auditory canals, with narrowing of the lower canals, unilateral cochlear and vestibular dysplasia, bilateral superior semicircular canal malformation, and bilateral absence of the posterior semicircular canals.

Conclusion:

To our knowledge, this is only the third such case described in the literature. Considering that the vestibulocochlear nerve has been unable to be demonstrated in almost all cases of duplicated internal auditory canal (unilateral and bilateral), our case supports the hypothesis that vestibulocochlear nerve aplasia or hypoplasia leads to internal auditory canal stenosis. We consider this rare presentation of bilateral narrow duplication of the internal auditory canal to represent a contraindication for cochlear implantation.

Keywords

Internal Auditory CanalSensorineural Hearing LossCongenital
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 124 , Issue 9 , September 2010 , pp. 1003 - 1006
Copyright
Copyright © JLO (1984) Limited 2010

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References

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