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Family Contexts, Parental Behaviour, and Personality Profiles of Children and Adolescents with Prader-Willi, Fragile-X, or Williams Syndrome

Published online by Cambridge University Press:  01 July 1998

Cornelis F. M. van Lieshout ,
Ronald E. De Meyer ,
Leopold M. G. Curfs  and
Jean-Pierre Fryns
Cornelis F. M. van Lieshout
Affiliation:
University of Nijmegen, The Netherlands
Ronald E. De Meyer
Affiliation:
University of Nijmegen, The Netherlands
Leopold M. G. Curfs
Affiliation:
Clinical Genetics Centre, Maastricht, The Netherlands
Jean-Pierre Fryns
Affiliation:
University of Leuven, Belgium
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Abstract

The personality profiles for youths with Prader-Willi, fragile-X, or Williams syndrome were compared to three matched groups attending regular schools. Using the California Child Q-Set (CCQ), both of the parents of the 39 children with Prader-Willi syndrome, 32 boys with fragile-X syndrome, 28 children with Williams syndrome, and children in the comparison groups provided independent personality descriptions in terms of the Big Five personality factors of Extraversion, Agreeableness, Conscientiousness, Emotional Stability, and Openness, along with Motor Activity and Irritability. Specific personality phenotypes for each of the three syndrome groups were found to be differentially related to parental behaviours (i.e. control and anger) and family contexts (i.e. experienced family stress, marital conflict, and parental consistency).

Keywords

Prader-Willi syndromefragile-X syndromeWilliams syndromeBig Five personality dimensionsparental behaviourfamily contextCalifornia Child Q-set
Type
Research Article
Information
The Journal of Child Psychology and Psychiatry and Allied Disciplines , Volume 39 , Issue 5 , July 1998 , pp. 699 - 710
Copyright
© 1998 Association for Child Psychology and Psychiatry

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