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Tricuspid atresia associated with aortopulmonary window: diagnostic and therapeutic dilemmas

Published online by Cambridge University Press:  29 September 2016

Vladimir Milovanovic ,
Igor Stefanovic  and
Slobodan Ilic
Vladimir Milovanovic*
Affiliation:
Department of Pediatric Cardiac Surgery, University Children’s Hospital, Belgrade, Serbia
Igor Stefanovic
Affiliation:
Department of Pediatric Cardiology, University Children’s Hospital, Belgrade, Serbia
Slobodan Ilic
Affiliation:
Department of Pediatric Cardiac Surgery, School of Medicine, University of Belgrade, Belgrade, Serbia
*
Correspondence to: V. Milovanovic, Department of Pediatric Cardiac Surgery, University Children’s Hospital, Tirsova 10, 11000 Belgrade, Serbia. Tel: +381 11 20 60 711; Fax: +381 11 26 84 672; E-mail: [email protected]
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Abstract

The association of tricuspid atresia with aortopulmonary window is exceptionally rare. We report a patient with tricuspid atresia, normally related great arteries, non-restrictive ventricular septal defect, and no pulmonary stenosis (type IC) with an aortopulmonary window who underwent successful initial surgical palliation. The unique anatomical feature of this case, other than the presence of the aortopulmonary window, was the absence of pulmonary stenosis at the level of either the ventricular septal defect or the pulmonary valve. All other reported cases have described some degree of restriction of anterograde pulmonary flow due to pulmonary stenosis or atresia.

Keywords

Tricuspid atresiaaortopulmonary windowstaged surgical palliation
Type
Brief Report
Information
Cardiology in the Young , Volume 27 , Issue 3 , March 2017 , pp. 580 - 583
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Copyright
© Cambridge University Press 2016 

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