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Surgical correction of a patient with discordant atrioventricular and concordant ventriculo-arterial connections

Published online by Cambridge University Press:  19 August 2008

Kiyozo Morita ,
Hiromi Kurosawa  and
Hisaki Miyamoto
Kiyozo Morita
Affiliation:
Jikei University School of Medicine, Department of Cardiovascular Surgery, Tokyo, Japan
Hiromi Kurosawa*
Affiliation:
Jikei University School of Medicine, Department of Cardiovascular Surgery, Tokyo, Japan
Hisaki Miyamoto
Affiliation:
Jikei University School of Medicine, Department of Cardiovascular Surgery, Tokyo, Japan
*
Hiromi Kurosawa, M.D. Department of Cardiac Surgery, Jikei Univ. School of Medicine, 3-19-18 Nishi-shinbashi, Minato-ku, Tokyo, 105, Japan. Tel 3-3433-1111; Fax: 3-3943-7515
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Abstract

The combination of discordant atrioventricular and concordant ventriculoarterial connections is an extremely rare entity, with only 8 cases of successful surgical repair being previously reported. Although from the clinical standpoint this anomaly is similar to complete transposition, this unusual combination is clearly suited by its morpho-physiological features to an atrial rather than an arterial switch procedure. A 17-year-old boy with this malformation, associated also with severe pulmonary hypertension, underwent a palliative Senning procedure, leaving the ventricular septal defect open and banding the pulmonary trunk. Postoperatively, hypoxemia was markedly improved, and was associated with a reduction of the level of pulmonary hypertension, contributing to marked symptomatic improvement.

Keywords

Senning procedurediscordant atriovencricular and concordant ventriculo-arterial connectionsventricular topology
Type
Brief-Reports
Information
Cardiology in the Young , Volume 7 , Issue 4 , October 1997 , pp. 442 - 445
Copyright
Copyright © Cambridge University Press 1997

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