Hostname: page-component-586b7cd67f-dsjbd Total loading time: 0 Render date: 2024-11-24T05:36:25.159Z Has data issue: false hasContentIssue false

Supravalvar stenosing tricuspid ring in congenitally corrected transposition

Published online by Cambridge University Press:  19 August 2008

Gordon Gladman
Affiliation:
Cardiology and Critical Care Medicine, The Hospital for Sick Children, University of Toronto, Toronto
Frank Casey
Affiliation:
Cardiology and Critical Care Medicine, The Hospital for Sick Children, University of Toronto, Toronto
Ian Adatia*
Affiliation:
Cardiology and Critical Care Medicine, The Hospital for Sick Children, University of Toronto, Toronto
*
Dr. Ian Adatia, Cardiology and Critical Care Medicine, The Hospital for Sick Children, Toronto, Canada, M5G 1X8. Tel. 416-813-6140; Fax. 416-813-7547.

Summary

We report an unusual case with discordant atrioventricular and ventriculoarterial connections. In addition to the commonly associated intracardiac anomalies ofventricular septal defect and subpulmonary tissue tags, a supravalvar ring was present above the left-sided, morphologically tricuspid valve. This case highlights the value of color flow Doppler echocardiography in making the diagnosis, particularly as the supravalvar ring was seen poorly angiographically.

Type
Brief Reports
Copyright
Copyright © Cambridge University Press 1996

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1.Chesler, E, Beck, W, Barnard, CN, Schrire, V. Supravalvular stenosing ring of the left atrium associated with corrected transposition of the great vessels. Am J Gardiol 1973; 31: 8488.CrossRefGoogle ScholarPubMed
2.Ritter, M, Schneider, J, Jenni, R, Supravalvular tricuspid ring and Ebstein”s anomaly incongenitally corrected transposition. Am J Cardiol 1992; 70: 16351636.CrossRefGoogle ScholarPubMed
3.Marino, B, Sanders, S, Parness, I, Golan, SObstruction of right ventricular inflow and outflow in corrected transposition of the great arteries {S,L,L}: two-dimensional echocardiographic diagnosis. J Am Coll Gardiol 1986; 8: 407411.CrossRefGoogle ScholarPubMed
4.Lundstrom, U, Bull, C, Wyse, R, Somerville, JThe natural and “unnatural” history of congenitally corrected transposition. Am J Cardiol 1990; 65: 12221229.CrossRefGoogle ScholarPubMed
5.Allwork, S, Bentall, H, Becker, A, Cameron, H, Gerlis, L, Wilkinson, J, Anderson, RCongenitally corrected transposition of the great arteries: morphologic study of 32 cases. Am J Cardiol 1976; 38: 910923.CrossRefGoogle ScholarPubMed
6.Shone, J, Sellers, R, Anderson, R, Adams, P, Lillehei, C, Edwards, JThe developmental complex of “parachute” mitral valve, supravalvular ring of left atrium, subaortic stenosis and coarctation of the aorta. Am J Cardiol 1963; 11: 714725.CrossRefGoogle Scholar
7.Craig, B, Smallhorn, J, Rowe, R, Williams, W, Trusler, G, Freedom, RSevere obstruction to systemic blood flow in congenitally corrected transposition (discordantatrioventricular and ventriculo-arterial connexions): an analysisof 14 patients. Int J Cardiol 1986; 11: 209217.CrossRefGoogle Scholar
8.Celermajer, D, Cullen, S, Deanfield, J, Sullivan, ICongenitally corrected transposition and Ebstein's anomaly of the systemic atriventricular valve: association with aortic arch obstruction. J Am Coll Cardiol 1991; 18: 10561058.CrossRefGoogle Scholar
9.Tulloh, RMR, Bull, C, Elliott, MJ, Sullivan, IDSupravalvar mitral stenosis: risk factors for recurrence or death after resection. Br Heart J 1995; 73: 164168.CrossRefGoogle ScholarPubMed
10.Folger, GSupravalvular tricuspid stenosis association with developmental abnormalities of the right heart and derivatives of the sixth aortic arch. Am J Cardiol 1968; 21: 8187.CrossRefGoogle ScholarPubMed