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Severe stenosis of a long tracheal segment, with agenesis of the right lung and left pulmonary arterial sling

Published online by Cambridge University Press:  03 February 2006

Hamish M. Munro ,
Andrea M. C. Sorbello  and
David G. Nykanen
Hamish M. Munro
Affiliation:
Department of Cardiovascular Anesthesia, The Congenital Heart Institute, Arnold Palmer Hospital for Women and Children/Miami Children's Hospital, Orlando, Florida, United States of America
Andrea M. C. Sorbello
Affiliation:
Department of Cardiology, The Congenital Heart Institute, Arnold Palmer Hospital for Women and Children/Miami Children's Hospital, Orlando, Florida, United States of America
David G. Nykanen
Affiliation:
Department of Cardiology, The Congenital Heart Institute, Arnold Palmer Hospital for Women and Children/Miami Children's Hospital, Orlando, Florida, United States of America
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Abstract

A baby presented at term with respiratory distress was managed with extracorporeal membrane oxygenation. Bronchoscopy revealed tracheal hypoplasia, complete tracheal rings, and agenesis of the right main bronchus. Echocardiography showed a left pulmonary arterial sling arising from the proximal part of the right pulmonary artery. Cardiac catheterization demonstrated abnormal pulmonary vasculature in the left lung which would have prevented survival, even after surgical repair. Diagnostic catheterization was important in delineating the anatomy, and aided in the decision not to proceed with surgical repair.

Keywords

Congenital heart diseasegreat vessel anomalieslung
Type
Brief Report
Information
Cardiology in the Young , Volume 16 , Issue 1 , January 2006 , pp. 89 - 91
Copyright
© 2006 Cambridge University Press

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