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Rheology of right ventricular outflow tract obstruction: sub-pulmonary membrane developing months after primary intervention to treat pulmonary atresia with intact interventricular septum

Part of: Cardiac Morphology Interventional Cardiology

Published online by Cambridge University Press:  31 May 2021

Baher M. Hanna Open the ORCID record for Baher M. Hanna [Opens in a new window] ,
Wesam E. El-Mozy  and
Sonia A. El-Saiedi
Baher M. Hanna*
Affiliation:
Division of Pediatric Cardiology, Department of Pediatrics, Cairo University, Cairo, Egypt
Wesam E. El-Mozy
Affiliation:
Department of Radiology, Cairo University, Cairo, Egypt
Sonia A. El-Saiedi
Affiliation:
Division of Pediatric Cardiology, Department of Pediatrics, Cairo University, Cairo, Egypt
*
Author for correspondence: Baher Hanna, MD, Tel: +201222441732.E-mail: [email protected]
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Abstract

Isolated sub-pulmonary membrane is a rare condition, the origin of which has been debatable. Transcatheter treatment of pulmonary valve atresia with intact interventricular septum by radiofrequency perforation and balloon dilatation to restore biventricular circulation is gaining more popularity, with improving results over time. We report in our experience of 79 cases in 10 years the development of a sub-pulmonary membrane in 4 cases: causing significant obstruction requiring surgical excision in one case that revealed a fibrous membrane on pathology; causing mild right ventricular outflow tract obstruction in another and not yet causing obstruction in 2. On cardiac MRI, the right ventricular outflow tract and the right ventricular outflow tract/pulmonary atresia angle showed no morphological abnormalities.

Keywords

Sub-pulmonary membranepulmonary atresiaradiofrequency perforation
Type
Original Article
Information
Cardiology in the Young , Volume 32 , Issue 1 , January 2022 , pp. 60 - 63
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Copyright
© The Author(s), 2021. Published by Cambridge University Press

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