Hostname: page-component-78c5997874-j824f Total loading time: 0 Render date: 2024-11-08T02:06:15.432Z Has data issue: false hasContentIssue false

Repair in infancy of right aortic arch with aberrant left brachiocephalic artery in the setting of a variant of the hypoplastic left heart syndrome

Published online by Cambridge University Press:  21 January 2005

Suvro S. Sett
Affiliation:
British Columbia Children's Hospital, Vancouver, BC, Canada
John B. Mawson
Affiliation:
British Columbia Children's Hospital, Vancouver, BC, Canada
George G. S. Sandor
Affiliation:
British Columbia Children's Hospital, Vancouver, BC, Canada

Abstract

A right aortic arch, with a retroesophageal transverse arch and an aberrant left brachiocephalic artery, is a rare anomaly by itself. When combined with severe mitral stenosis and hypoplasia of the left ventricle, it is rarer still. We describe the diagnosis and treatment of this rare anomaly in an infant using a modification of the Norwood operation.

Type
Brief Report
Copyright
© 2004 Cambridge University Press

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

Shuford WD, Sybers RG, Hogan GB. Type 4 right aortic arch (aberrant left innominate artery). In: Shuford WH (ed.). The Aortic Arch and Its Malformations with Emphasis on the Angiographic Features. Charles C. Thomas, Springfield, IL, 1974, pp 6972.
Moes CAF, Mawson JB, MacDonald C, Smallhorn J. Right aortic arch with retroesophageal left aberrant innominate artery. Pediatr Cardiol 1996; 17: 402406.Google Scholar
Edwards JE. Malformations of the aortic arch system manifested as “vascular rings”. Lab Invest 1953; 2: 5675.Google Scholar
Kishimoto H, Kawahira Y, Kawata H, Miune T, Iwai S, Mori T. The modified Norwood palliation on a beating heart. J Thorac Cardiovasc Surg 1999; 118: 11301132.Google Scholar
Duncan BW, Rosenthal GL, Jones TK, Lupinetti FM. First-stage palliation of complex univentricular cardiac anomalies in older infants. Ann Thorac Surg 2001; 72: 20772080.Google Scholar
Gil-Juarena JM, Murtra M, Goncalves A, Miro L. Aortic coarctation, vascular ring, and right aortic arch with aberrant subclavian artery. Ann Thorac Surg 2002; 73: 16401642.Google Scholar
Kanter KR, Erez E, Williams WH, Tam VK. Extra-anatomic aortic bypass via sternotomy for complex aortic arch stenosis in children. J Thorac Cardiovasc Surg 2000; 120: 885890.Google Scholar