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Rare presentation of eosinophilic granulomatosis polyangiitis with left ventricular endomyocardial fibrosis in a child

Published online by Cambridge University Press:  16 May 2022

Vinoth Doraiswamy Open the ORCID record for Vinoth Doraiswamy [Opens in a new window] ,
Sivakumar Vengudusamy  and
Jayavardhana Arumugam
Vinoth Doraiswamy*
Affiliation:
Department of Cardiology, PSG Institute of Medical Sciences and Research, Peelamedu, Coimbatore 641004, Tamil Nadu, India
Sivakumar Vengudusamy
Affiliation:
Department of Rheumatology, PSG Institute of Medical Sciences and Research, Peelamedu, Coimbatore 641004, Tamil Nadu, India
Jayavardhana Arumugam
Affiliation:
Department of Pediatrics, PSG Institute of Medical Sciences and Research, Peelamedu, Coimbatore 641004, Tamil Nadu, India
*
Address for correspondence: Vinoth Doraiswamy, MD, FNB (Pediatric Cardiology), Consultant Pediatric Cardiologist, Department of Cardiology, PSG Institute of Medical Sciences and Research, Peelamedu, Coimbatore 641004, Tamil Nadu, India. Tel: +91-422-2570170, +91-422-4345353. E-mail: [email protected]
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Abstract

Eosinophilic granulomatosis polyangiitis represents less than 2% of vasculitis cases in childhood. Children have worse long-term outcomes and higher mortality. Cardiac involvement portends a worse prognosis. We describe here an adolescent girl who presented with heart failure and stroke. Her blood investigations showed eosinophilia and high IgE levels. Cardiac evaluation revealed myocarditis, intracardiac thrombus, and endomyocardial fibrosis, a rare presentation of this disease in childhood.

Keywords

EGPAendomyocardial fibrosismural thrombuscardioembolic stroke
Type
Brief Report
Information
Cardiology in the Young , Volume 33 , Issue 1 , January 2023 , pp. 153 - 155
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Copyright
© The Author(s), 2022. Published by Cambridge University Press

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