Hostname: page-component-586b7cd67f-t7fkt Total loading time: 0 Render date: 2024-11-24T11:26:00.380Z Has data issue: false hasContentIssue false
  • English
  • Français

Pulmonary atresia with intact ventricular septum, right-sided aortic arch, and an aorto-pulmonary collateral artery

Published online by Cambridge University Press:  19 August 2008

Chandrakant R. Patel ,
Michael L. Spector  and
Kenneth G. Zahka
Chandrakant R. Patel*
Affiliation:
Department of Pediatrics, Division of Pediatric Cardiology, and Department of Cardiothoracic Surgery, Rainbow Babies and Children's Hospital, Case Western Reserve University School of Medicine, Cleveland, OH, USA
Michael L. Spector
Affiliation:
Department of Pediatrics, Division of Pediatric Cardiology, and Department of Cardiothoracic Surgery, Rainbow Babies and Children's Hospital, Case Western Reserve University School of Medicine, Cleveland, OH, USA
Kenneth G. Zahka
Affiliation:
Department of Pediatrics, Division of Pediatric Cardiology, and Department of Cardiothoracic Surgery, Rainbow Babies and Children's Hospital, Case Western Reserve University School of Medicine, Cleveland, OH, USA
*
Chandrakant R Patel, MBBS, Rainbow Babies and Childrens Hospital, Case Western Reserve University, 11100 Euclid Avenue, Cleveland, OH 44106, USA. Tel: +1 (216) 8443275; fax: +1 (216) 844478.
Get access Rights & Permissions [Opens in a new window]

Abstract

Described is a rare association in a patient with the heart in the left chest, namely pulmonary atresia with intact ventricular septum, fistulous coronary arterial connections, a right-sided aortic arch and an aorto-pulmonary collateral artery feeding one lung. The pulmonary arteries were non-confluent, with the right lung supplied by the right arterial duct originating from the under surface of the right-sided aortic arch, and the left lung supplied through the aorto-pulmonary collateral artery arising from the descending aorta. The surgical management is different in the setting of non-confluent pulmonary arteries.

Keywords

Pulmonary atresia with intact ventricular septumaorto-pulmonary collateral arteryright-sided aortic arch
Type
Brief Reports
Information
Cardiology in the Young , Volume 9 , Issue 5 , September 1999 , pp. 512 - 515
Copyright
Copyright © Cambridge University Press 1999

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1.Hanley, FL, Sade, RM, Blackstone, EH, Kirklin, JW, Freedom, RM, Nanda, NC. Outcomes in neonatal pulmonary atresia with intact ventricular septum. A multi-institutional study. J Thorac Cardiovasc Surg 1993; 105: 406–427.CrossRefGoogle Scholar
2.Giglia, TM, Mandell, VS, Connor, AR, Mayer, JE, Lock, JE. Diagnosis and management of right ventricle-dependent coronary circulation in pulmonary atresia with intact ventricular septum. Circulation 1992; 86: 1516–1528.Google Scholar
3.Bull, C, Kostelka, M, Sorensen, K, de Leval, M. Outcome measures for the neonatal management of pulmonary atresia with intact ventricular septum. J Thorac Cardiovasc Surg 1994; 107: 359–366.CrossRefGoogle ScholarPubMed
4.Thiene, G, Frescura, C, Bortolotti, U, Del Maschio, A, Valente, M. The systemic pulmonary circulation in pulmonary atresia with ventricular septal defect: concept of reciprocal development the fourth and sixth aortic arches. Am Heart J 1981; 101: 339–344.CrossRefGoogle ScholarPubMed
5.Mildner, RJ, Kiraly, L, Sreeram, N. Pulmonary atresia, ‘intact ventricular septum’, and aorto-pulmonary collateral arteries. Heart 1997; 77: 173–175.CrossRefGoogle Scholar
6.Luciani, GB, Swilley, S, Starnes, VA. Pulmonary atresia, intact ventricular septum, and major aorto-pulmonary collaterals: morphogenetic and surgical implications. J Thorac Cardiovasc Surg 1995; 110: 853–854.CrossRefGoogle Scholar
7.Milanesi, O, Daliento, L, Thiene, G. Solitary aorta with bilateral ductal origin of non-confluent pulmonary arteries in pulmonary atresia with intact ventricular septum. Int J Cardiol 1990; 29: 90–92.Google Scholar