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Pulmonary atresia with intact ventricular septum and congenital left ventricular aneurysm

Part of: Cardiac Morphology

Published online by Cambridge University Press:  22 April 2018

Benton Ng ,
Rhiannon Hickok ,
Gary Stapleton  and
Tom Karl
Benton Ng*
Affiliation:
Johns Hopkins All Children’s Hospital, Saint Petersburg, FL, USA
Rhiannon Hickok
Affiliation:
Johns Hopkins All Children’s Hospital, Saint Petersburg, FL, USA
Gary Stapleton
Affiliation:
Johns Hopkins All Children’s Hospital, Saint Petersburg, FL, USA
Tom Karl
Affiliation:
Johns Hopkins All Children’s Hospital, Saint Petersburg, FL, USA
*
Author for correspondence: B. Ng, Johns Hopkins All Children’s Hospital, 601 5th St S, Saint Petersburg, FL 33701-4816, USA. Tel: 727 767 3333; Fax: 727 767 8990; E-mail: [email protected]
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Abstract

Pulmonary atresia with intact ventricular septum and congenital left ventricular aneurysms are both rare, representing <1 and <0.1% of CHD, respectively. The association of left ventricular aneurysms and pulmonary atresia with intact ventricular septum has been documented in the literature, but all the previous case reports have involved children with acquired left ventricular aneurysms. We report an interesting case of a child with both pulmonary atresia with intact ventricular septum and a congenital left ventricular aneurysm. The combination of these two lesions ultimately affected the course of clinical care for the patient.

Keywords

Pulmonary atresialeft ventricular aneurysmCHDgeneral cardiology
Type
Brief Report
Information
Cardiology in the Young , Volume 28 , Issue 6 , June 2018 , pp. 876 - 878
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Copyright
© Cambridge University Press 2018 

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References

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