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Pulmonary atresia with intact ventricular septum and antenatal left ventricular failure

Published online by Cambridge University Press:  21 January 2005

Saad Khoshhal ,
George G. S. Sandor  and
Walter J. Duncan
Saad Khoshhal
Affiliation:
Department of Pediatrics, Division of Cardiology, British Columbia Children's Hospital, Vancouver, Canada
George G. S. Sandor
Affiliation:
Department of Pediatrics, Division of Cardiology, British Columbia Children's Hospital, Vancouver, Canada
Walter J. Duncan
Affiliation:
Department of Pediatrics, Division of Cardiology, British Columbia Children's Hospital, Vancouver, Canada
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Abstract

Pulmonary atresia with intact ventricular septum has been described extensively, and it is recognized that associated abnormalities of the coronary arteries may cause ischemia. We describe a fetus, diagnosed antenatally as having pulmonary atresia with intact ventricular septum and severe hypoplasia of the right ventricle, who developed severe left ventricular dysfunction. We hypothesize that this is due to reduced coronary blood flow because of falling right ventricular volume in the presence of complete right ventricular coronary arterial dependence.

Keywords

Pulmonary atresiaantenatal left heart failure
Type
Brief Report
Information
Cardiology in the Young , Volume 14 , Issue 3 , June 2004 , pp. 335 - 337
Copyright
© 2004 Cambridge University Press

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References

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