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The novel use of an advanced thrombectomy system to manage a complex pericardial effusion associated with kaposiform lymphangiomatosis

Published online by Cambridge University Press:  31 March 2023

Natalie Soszyn Open the ORCID record for Natalie Soszyn [Opens in a new window] ,
Ryan Leahy  and
Gareth J. Morgan
Natalie Soszyn*
Affiliation:
Division of Cardiology, Department of Pediatrics, Heart Institute, Children’s Hospital Colorado, University of Colorado Denver | Anschutz Medical Campus, 13123 E 16th Ave, Aurora, CO 80045-2560, USA
Ryan Leahy
Affiliation:
Division of Cardiology, Department of Pediatrics, Heart Institute, Children’s Hospital Colorado, University of Colorado Denver | Anschutz Medical Campus, 13123 E 16th Ave, Aurora, CO 80045-2560, USA
Gareth J. Morgan
Affiliation:
Division of Cardiology, Department of Pediatrics, Heart Institute, Children’s Hospital Colorado, University of Colorado Denver | Anschutz Medical Campus, 13123 E 16th Ave, Aurora, CO 80045-2560, USA
*
Author for correspondence: Dr. Natalie Soszyn, Children’s Hospital Colorado, 13123 East 16th Avenue, Box 100, Aurora, CO 80045, USA. Tel: +1 (720) 777 1234. E-mail: [email protected]
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Abstract

A 4-year-old boy presented to our institution with pancytopenia, consumptive coagulopathy, hepatosplenomegaly and recurrent complex pericardial effusion secondary to kaposiform lymphagiomatosis. Due to extensive loculation, conventional drainage was minimally effective. As an adjunct to medical therapy, the Indigo™ aspiration system was used to remove thrombus within the pericardial space. Our patient had good medium-term results with complete resolution of his pericardial effusion at 4 months.

Keywords

Pericardial effusionKaposiform Lymphangiomatosisthrombectomy
Type
Brief Report
Information
Cardiology in the Young , Volume 33 , Issue 9 , September 2023 , pp. 1760 - 1762
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Copyright
© The Author(s), 2023. Published by Cambridge University Press

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References

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