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Non-cardiac cyanosis in left isomerism—report of two cases of multiple pulmonary arteriovenous malformations
Published online by Cambridge University Press: 19 August 2008
Summary
Isomerism of the left atrial appendages is often associated with cyanosis due to intracardiac structural abnormalities such as common atrium and/or anomalous pulmonary or systemic venous connections. We report two cases of children with cyanosis and left isomerism but no other lesions within the heart. In these cases, multiple small pulmonary arteriovenous malformations were found bilaterally, resulting in intrapulmonary right-to-left shunting and systemic desaturation.
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