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Neonatal hemodynamics in patients with hypoplastic left heart syndrome

Published online by Cambridge University Press:  21 September 2005

James C. Huhta
James C. Huhta
Affiliation:
Department of Pediatrics, Congenital Heart Institute of Florida and University of South Florida/All Children's Hospital, University of South Florida, Tampa, Florida, USA
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Extract

The neonate with hypoplastic left heart syndrome presents a challenge for clinical diagnosis and management. Three diagnostic goals must be met. First, it is necessary to make an etiologic cardiac diagnosis so as to rule out any genetic abnormality. Second, the anatomic cardiac diagnosis is made by segmental echocardiographic analysis, including details of the atrial arrangement, venous return, the patency of the arterial duct, atrial anatomy, and the arrangement of the aortic arch. Finally, the physiologic cardiac diagnosis is made by Doppler evaluation. In some patients, the diagnosis of hypoplastic left heart syndrome is not synonymous with functionally univentricular physiology, and a bi-ventricular repair can be achieved.1

Type
Clinical Aspects
Information
Cardiology in the Young , Volume 14 , Issue S1 , February 2004 , pp. 22 - 26
Copyright
© 2004 Cambridge University Press

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References

Nurozler F, Bradley SM. Considerations in biventricular repair after the Norwood procedure. Eur J Cardiothorac Surg 2000; 18: 540–544.Google Scholar
Brackley KJ, Kilby MD, Wright JG, et al. Outcome after prenatal diagnosis of hypoplastic left-heart syndrome: a case series. Lancet 2000; 356: 1143–1147.Google Scholar
Daebritz SH, Tiete AR, Rassoulian D, et al. Borderline hypoplastic left heart malformations: Norwood palliation or two-ventricle repair? Thorac Cardiovasc Surg 2002; 50: 266–270.Google Scholar
Schwartz ML, Gauvreau K, Geva T. Predictors of outcome of biventricular repair in infants with multiple left heart obstructive lesions. Circulation 2001; 104: 682–687.Google Scholar
Falkensammer CB, Paul J, Huhta JC. Fetal congestive heart failure: Correlation of Tei-Index and Cardiovascular-Score. J Perinat Med 2001; 29: 390–398.Google Scholar
Mahle WT, Clancy RR, McGaurn SP, Goin JE, Clark BJ. Impact of prenatal diagnosis on survival and early neurologic morbidity in neonates with the hypoplastic left heart syndrome. Pediatrics 2001; 107: 1277–1282.Google Scholar
Rychik J, Bush DM, Spray TL, Gaynor JW, Wernovsky G. Assessment of pulmonary/systemic blood flow ratio after first-stage palliation for hypoplastic left heart syndrome: development of a new index with the use of Doppler echocardiography. J Thorac Cardiovasc Surg 2000; 120: 81–87.Google Scholar
Lemler MS, Zellers TM, Harris KA, Ramaciotti C. Coarctation index: identification of recurrent coarctation in infants with hypoplastic left heart syndrome after the Norwood procedure. Am J Cardiol 2000; 86: 697–699, A9.Google Scholar
Paul JJ H.G., Morell V, Cook JR, Huhta JC. Non-geometric RV Function Assessment After Stage I Norwood for HLHS. Abstract presented at the International Meeting of the Latin American Cardiology Society, Miami, September 2000.
Drinkwater DC Jr, Aharon AS, Quisling SV, et al. Modified Norwood operation for hypoplastic left heart syndrome. Ann Thorac Surg 2001; 72: 2081–2087.Google Scholar