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Natural history of complex transposition of great arteries in an adult: a case report

Part of: Transposition of Great Arteries

Published online by Cambridge University Press:  16 May 2019

Jahir Fresnel Narcisse-Alvarez ,
Susan Cristina Pumacayo-Cardenas  and
Nilda Espinola-Zavaleta Open the ORCID record for Nilda Espinola-Zavaleta [Opens in a new window]
Jahir Fresnel Narcisse-Alvarez
Affiliation:
Department of Nuclear Cardiology, National Institute of Cardiology Ignacio Chavez, Mexico City, Mexico
Susan Cristina Pumacayo-Cardenas
Affiliation:
Department of Magnetic Resonance Imaging, National Institute of Cardiology Ignacio Chavez, Mexico City, Mexico
Nilda Espinola-Zavaleta*
Affiliation:
Department of Nuclear Cardiology, National Institute of Cardiology Ignacio Chavez, Mexico City, Mexico Department of Echocardiography, ABC Medical Center, Mexico City, Mexico
*
Author for correspondence: Nilda Espinola-Zavaleta, MD, PhD, National Institute of Cardiology Ignacio Chavez, Juan Badiano No. 1, Colonia Seccion XVI, Tlalpan, P.C. 14080, Mexico City, Mexico. Tel: +5255 55732911; E-mail: [email protected] Fax number: +52556063931
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Abstract

Background:

Transposition of the great arteries is the most common cyanotic cardiac lesion in newborns. Transposition of the great arteries without surgical correction is fatal during the first year of life. Contemporary outcome studies have shown that survival rates after surgery are excellent and most patients live to adulthood.

Case summary:

Woman with complex transposition of the great arteries with atrial and ventricular septal defects and subvalvular and valvular pulmonary stenosis, who has survived until the age of 31 years without surgery. The diagnosis was made by echocardiography and cardiac magnetic resonance. She underwent successful corrective surgical treatment after this age, by means of a Jatene operation.

Conclusion:

In transposition of the great arteries patients, a high index of cases dies in the first month of life. Our case represents a natural history of the complex transposition of the great arteries. Non-invasive imaging studies are very useful for the diagnosis and follow-up of patients with transposition of the great arteries, especially echocardiography and cardiac magnetic resonance. In our case, the multimodality approach and the corrective surgery allowed her to survive.

Keywords

Transposition of great arteriesadulthoodJatene operationcardiac magnetic resonanceechocardiography
Type
Brief Report
Information
Cardiology in the Young , Volume 29 , Issue 5 , May 2019 , pp. 720 - 724
Copyright
© Cambridge University Press 2019 

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