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Myotonic dystrophy presenting as atrial flutter in childhood

Published online by Cambridge University Press:  20 January 2005

Kenji Suda ,
Masahiko Matsumura  and
Yuji Hayashi
Kenji Suda
Affiliation:
Division of Pediatric Cardiology, Department of Pediatrics, Tenri Hospital, Tenri City, Japan
Masahiko Matsumura
Affiliation:
Division of Pediatric Cardiology, Department of Pediatrics, Tenri Hospital, Tenri City, Japan
Yuji Hayashi
Affiliation:
Department of Internal medicine, Kinan Hospital, Mihama town, Mie, Japan
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Abstract

A 12-year-old boy presented with tachycardia and cardiomegaly. An electrocardiogram showed atrial flutter with a ventricular rate of 170 beats/min. The echocardiogram showed left ventricular dilation, with decreased contractility. Electromyography confirmed the diagnosis of myotonic dystrophy. The atrial flutter was converted to sinus rhythm by electroversion, leading to restoration of normal cardiac function. Our case illustrates that atrial flutter can be an early sign of the cardiac complications of myotonic dystrophy in childhood.

Keywords

Paediatricsatrial arrhythmiascardiomyopathy
Type
Brief Report
Information
Cardiology in the Young , Volume 14 , Issue 1 , February 2004 , pp. 89 - 92
Copyright
© 2004 Cambridge University Press

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