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Leftward deviation of the primary septum or dividing left atrial shelf?

Part of: Cardiac Morphology

Published online by Cambridge University Press:  09 November 2021

Jelena Hubrechts Open the ORCID record for Jelena Hubrechts [Opens in a new window] ,
Julie Pollenus  and
Marc Gewillig
Jelena Hubrechts*
Affiliation:
Department of Congenital and Pediatric Cardiology, University Hospital Saint-Luc, Brussels, Belgium
Julie Pollenus
Affiliation:
Department of Pediatrics, University Hospital Leuven, Leuven, Belgium
Marc Gewillig
Affiliation:
Department of Congenital and Pediatric Cardiology, University Hospital Leuven, Leuven, Belgium
*
Author for correspondence: J. Hubrechts, MD, Pediatric and Congenital Cardiology, University Hospital Saint-Luc, Avenue Hippocrate 10, Brussels B-1200, Belgium. Tel: +32 2 764 16 59. Fax: +32 2 764 89 11. E-mail: [email protected]
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Abstract

Isolated leftward prolapse or deviation of the primary atrial septum is a rare CHD that can mimic abnormal pulmonary venous return at first sight. We present a case of a newborn infant, referred for surgical correction of totally anomalous pulmonary venous return into the right atrium, with the peri-operative finding of a leftward deviation of the superior margin of the primary atrial septum. The distinction with a dividing atrial shelf could not be confirmed with certainty. Fifty-three similar cases from the literature are incorporated. A detailed review of the current account on atrial septation is studied. The embryological and clinical features of a dividing partition of the left atrium are discussed.

Keywords

Primary septumdeviationdivided left atriumatrial septal development
Type
Review
Information
Cardiology in the Young , Volume 31 , Issue 12 , December 2021 , pp. 1893 - 1900
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Copyright
© The Author(s), 2021. Published by Cambridge University Press

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